The Korean journal of internal medicine

The Korean Association of Internal Medicine (대한내과학회)
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Ewing's Sarcoma of the Lesser Sac Masquerading as a Pancreatic Tumor

  • Rao, Lakshmi (Department of Pathology, Kasturba Medical College) ;
  • Monappa, Vidya (Department of Pathology, Kasturba Medical College) ;
  • Rodrigues, Gabriel (Department of Surgery, Kasturba Medical College and Kasturba Hospital) ;
  • Suresh, B.P. (Department of Surgery, Kasturba Medical College and Kasturba Hospital)
  • Published : 2012.03.01
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Abstract

Extraosseous Ewing's sarcoma/primitive neuroectodermal tumor (ES/PNET) is an uncommon, aggressive, and malignant tumor with a poor patient outcome. Its occurrence in the lesser sac is a rare event and to the best of our knowledge, has not been previously described. The present case was clinically and radiologically misdiagnosed as a pancreatic tumor/gastrointestinal stromal tumor. Histopathology revealed a tumor with "small round cells" that were positive for CD99, confirming the diagnosis of ES/PNET. This report highlights the importance of considering Ewing's sarcoma in the differential diagnosis of intraabdominal, extraintestinal masses.

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References

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Cited by

  1. Extra-osseous Ewing sarcoma of the pancreas: case report with radiologic, pathologic, and molecular correlation, and brief review of the literature vol.473, pp.3, 2012, https://doi.org/10.1007/s00428-018-2344-y
  2. Intraabdominal lesser sac metastasis from Ewing’s sarcoma: An exceptional localization vol.9, pp.None, 2012, https://doi.org/10.1177/2050313x211022426