The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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Tracheobronchomegaly with Bronchomalacia

기관기관지거대증 환자 1예

  • Lee, Jun-Hee (Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Park, Hye-Yon (Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Lee, Min-Ji (Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Lee, Yoon-Jung (Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Ahn, Joon-Seong (Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Jeon, Ja-Ryong (Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Kim, Ho-Joong (Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • 이준희 (성균관대학교 의과대학 삼성서울병원 내과) ;
  • 박혜연 (성균관대학교 의과대학 삼성서울병원 내과) ;
  • 이민지 (성균관대학교 의과대학 삼성서울병원 내과) ;
  • 이윤정 (성균관대학교 의과대학 삼성서울병원 내과) ;
  • 안준성 (성균관대학교 의과대학 삼성서울병원 내과) ;
  • 전자룡 (성균관대학교 의과대학 삼성서울병원 내과) ;
  • 김호중 (성균관대학교 의과대학 삼성서울병원 내과)
  • Published : 2012.09.01
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Abstract

Tracheobronchomegaly, or Mounier-Kuhn syndrome, is a rare clinical and radiologic condition characterized by marked tracheobronchial dilatation and recurrent lower respiratory tract infections. It is thought to be due to a congenital anomaly. A diagnosis is typically made using computed tomography (CT) and bronchoscopy. Symptoms can range from minimal with preserved lung function to severe respiratory failure. Here, we present the case of a 50-year-old male who was referred to our hospital for chronic cough, sputum, and dyspnea. In addition, the patient showed tracheobronchomegaly with bronchomalacia on CT and bronchoscopy. This report describes a rare case of Mounier-Kuhn syndrome with a literature review.

저자들은 만성 기침과 객담, 호흡곤란을 호소하는 환자에서 기관지연화증을 동반한 기관기관지거대증을 진단하였기에 그 사례를 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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