Mayer-Rokitansky-Kuster-Hauser 증후군 환자에서 회음부 복강경하 직결장질성형술을 이용한 질의 재건: 증례보고

Vaginal Reconstruction with Laparoscopic-perineal Rectosigmoid Colpopoiesis in Mayer-Rokitansky-Kuster-Hauser Syndrome: A Case Report

  • 배성근 (경북대학교 의학전문대학원 성형외과학교실) ;
  • 이상윤 (경북대학교 의학전문대학원 성형외과학교실) ;
  • 조병채 (경북대학교 의학전문대학원 성형외과학교실) ;
  • 최규석 (경북대학교 의학전문대학원 외과학교실)
  • Bae, Sung-Gun (Department of Plastic and Reconstructive Surgery, Kyungpook National University) ;
  • Lee, Sang-Yun (Department of Plastic and Reconstructive Surgery, Kyungpook National University) ;
  • Cho, Byung-Chae (Department of Plastic and Reconstructive Surgery, Kyungpook National University) ;
  • Choi, Kyu-Seok (Department of Surgery, College of Medicine, Kyungpook National University)
  • 투고 : 2009.07.09
  • 심사 : 2011.03.17
  • 발행 : 2011.05.10

초록

Purpose: Various operations have been proposed to compensate for congenital absence of the vagina using ileal or colonic interposition. These methods involve laparotomy, which shows postoperative complications such as long scar and delayed recovery. One case of neovagina reconstruction with laparoscopic rectosigmoid colpopoiesis in Mayer-Rokitansky-Kuster-Hauser syndrome is presented to avoid laparotomic complications. Methods: Laparoscopic surgery was performed in a 27-year-old MRKH syndrome patient. After a cruciate incision, blunt dissection through two-finger wide space was created between the bladder and the rectum. A 14-cm rectosigmoid segment vascularized by a branch of sigmoid artery was isolated by laparoscopy. The distal end was sutured with vaginal vestibule mucosa. A continuity of intestine was restored by circular end-to-end proximate curved intraluminal stapler CDH29$^{(R)}$ through perineal opening. Results: Total operation time was 4 hr 15 min. Normal walking and ingestion were possible within 3 days and 4 days after surgery. The hospital stay was 7 days and the patient was followed up for 6 months. The neovaginal introitus was wide enough for inserting two fingers, and there has been no narrowing of the neovagina on palpation as confirmed by vaginogram. The patient had functional self-lubricating neovagina without excessive mucous production or the need for routine dilation or unnoticeable scar. Conclusion: The successful result of this laparoscopic vaginal reconstruction technique with rectosigmoid segment suggests that this technique can be considered for the option of vaginal reconstruction in girls with the MRKH syndrome.

키워드

참고문헌

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