Tuberculosis and Respiratory Diseases

  • 제71권2호
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  • Pages.126-133
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  • 2011
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  • 1738-3536(pISSN)
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  • 2005-6184(eISSN)
대한결핵및호흡기학회 (The Korean Academy of Tuberculosis and Respiratory Diseases)
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Isolated Right Pulmonary Artery Hypoplasia with Retrograde Blood Flow in a 68-Year Old Man

  • Chang, You-Jin (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Ra, Seung-Won (Department of Internal Medicine, Ulsan University Hospital, University of Ulsan College of Medicine) ;
  • Chae, Eun-Jin (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Seo, Joon-Beom (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Won-Young (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Na, Shin (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Joo-Hee (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Park, Tai-Sun (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Park, Soo-Kyung (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Park, Seong-Joon (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lee, Tae-Hoon (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Ahn, Young-Chel (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lee, Sang-Do (Department of Pulmonary and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine)
  • 투고 : 2011.07.19
  • 심사 : 2011.08.03
  • 발행 : 2011.08.30
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초록

Unilateral pulmonary artery hypoplasia (UPAH) is a rare disease in adults and is frequently accompanied by a congenital cardiac anomaly at a young age. The diagnosis is usually based on computed tomography (CT), angiography, and magnetic resonance imaging (MRI). However, no reports are available on retrograde flow in patients with UPAH. We describe a 68-year-old man with isolated UPAH and retrograde blood flow. He was admitted for dyspnea on exertion for the past 23 years. His diagnosis was delayed, as his symptoms and signs mimicked his underlying pulmonary diseases, such as emphysema and previous tuberculous pleurisy sequelae. A discrepancy was detected between the results of a ventilation-perfusion scan and the CT image. This was resolved by MRI, which showed retrograde blood flow from the right to the left pulmonary artery. Using MRI, we diagnosed this patient with isolated pulmonary artery hypoplasia and retrograde flow.

키워드

참고문헌

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피인용 문헌

  1. Isolated Peripheral Pulmonary Artery Hypoplasia in Adulthood Presented with Occasional Hemoptysis vol.196, pp.9, 2011, https://doi.org/10.1164/rccm.201704-0726im
  2. Isolated Unilateral Pulmonary Artery Hypoplasia with Accompanying Pulmonary Parenchymal Findings on CT: A Case Report vol.76, pp.5, 2011, https://doi.org/10.3348/jksr.2017.76.5.369
  3. Isolated absence of right pulmonary artery in a 4-year old child: a case report vol.11, pp.None, 2018, https://doi.org/10.2147/imcrj.s181571
  4. Congenital isolated unilateral hypoplasia of the left pulmonary artery: A rare incidental anomaly in an elderly female vol.38, pp.1, 2011, https://doi.org/10.4103/lungindia.lungindia_103_20
  5. Congenital isolated unilateral agenesis of pulmonary arteries in adults: case series and review vol.37, pp.suppl1, 2021, https://doi.org/10.1007/s12055-020-01032-w