Primary Epidural Peripheral Primitive Neuroectodermal Tumor of the Lumbar Spine: A Case Report

요추에 발생한 원발성 말초형 경막 외 원시신경외배엽종양: 증례 보고

  • Choi, Woo-Jung (Department of Radiology, Hanyang University Hospital) ;
  • Lee, Seung-Hun (Department of Radiology, Hanyang University Hospital) ;
  • Joo, Kyung-Bin (Department of Radiology, Hanyang University Hospital) ;
  • Paik, Seung-Sam (Department of Pathology, Hanyang University Hospital) ;
  • Lee, Young-Ho (Department of Pediatrics, Hanyang University Hospital) ;
  • Jun, Young-Jin (Department of Pathology, Hanyang University Hospital)
  • 최우정 (한양대의료원 영상의학과) ;
  • 이승훈 (한양대의료원 영상의학과) ;
  • 주경빈 (한양대의료원 영상의학과) ;
  • 백승삼 (한양대의료원 병리과) ;
  • 이영호 (한양대의료원 소아과) ;
  • 전영진 (한양대의료원 병리과)
  • Published : 2011.05.01

Abstract

A primitive neuroectodermal tumor (PNET) is a highly malignant tumor in children and young adults, and extremely rare in the spine. We report a case of a primary epidural peripheral PNET of the lumbar spine. The present extremely rare case of primary epidural peripheral PNET of the lumbar spine illustrates the unexpected occurrence and should be included in differential diagnoses for patients with spinal tumors.

원시신경외배엽종양은 소아와 젊은 성인에서 발생하는 고도의 악성종양으로 척추에서는 매우 드물게 발생한다. 저자들은 요추에 발생한 원발성 말초형 경막 외 원시신경외배엽종양 증례를 경험하였기에 이를 보고하고자 한다. 원발성 말초형 원시신경외배엽종양은 매우 드문 증례로 예기치 않게 발생하며 척추종양이 있는 환자에서 감별진단에 포함되어야 한다.

Keywords

References

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