Spontaneous Regression of an Intraabdominal Desmoid Tumor in a Patient with Total Gastrectomy

전위절제술 후 발생한 복강내 유건종의 자연소실

  • Moon, In-Kyu (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Kim, Tae-Hyo (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Jang, Hyun-Jeong (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Kim, Wan-Soo (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Hwang, Jae-Jin (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Jung, Woon-Tae (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Lee, Ok-Jae (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine)
  • 문인규 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 김태효 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 장현정 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 김완수 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 황재진 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 정운태 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 이옥재 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원)
  • Published : 2011.10.01

Abstract

Desmoid tumor is rare neoplasm characterized by clonal proliferation of myofibroblasts that do not metastasise, but often exhibit an infiltrative pattern and functional impairment. The etiology of this tumor is unknown, but hormonal, genetic, and physical factors play a role in its development and growth. The clinical behavior and natural history of desmoid tumors remains unpredictable and enigmatic. However, spontaneous regression of desmoid tumors is rare. Here we report spontaneous regression of an intraabdominal desmoid tumor in a patient who underwent total gastrectomy.

유건종은 근초나 근건막 연조직에서 유래하는 양성 섬유종증으로 매우 드물다. 원인은 밝혀지지 않았으나 수술을 포함한 외상, 에스트로겐, 유전적 결함 등이 관여한다고 알려져 있다. 저자들은 진행성 위암으로 인한 전위절제술 이후 복강 내 종괴가 발생하여 시행한 수술에서 유건종으로 진단되었으나 제거치 못하고 경과관찰 중 자연소실을 경험하였기에 문헌고찰과 함께 보고한다.

Keywords

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