A Solid Pseudopapillary Tumor Presenting as Hematemesis

토혈을 주소로 내원한 고형 가유두상 종양 1예

  • Cheon, Woong (Department of Internal Medicine, Inha University College of Medicine) ;
  • Kim, Joon-Mee (Department of Pathology, Inha University College of Medicine) ;
  • Bang, Byoung-Wook (Department of Internal Medicine, Inha University College of Medicine) ;
  • Lee, Don-Haeng (Department of Internal Medicine, Inha University College of Medicine) ;
  • Han, Jee-Young (Department of Internal Medicine, Inha University College of Medicine) ;
  • Shin, Yong-Woon (Department of Internal Medicine, Inha University College of Medicine) ;
  • Kim, Young-Soo (Department of Internal Medicine, Inha University College of Medicine)
  • 천웅 (인하대학교 의과대학 내과학교실) ;
  • 김준미 (인하대학교 의과대학 병리학교실) ;
  • 방병욱 (인하대학교 의과대학 내과학교실) ;
  • 이돈행 (인하대학교 의과대학 내과학교실) ;
  • 한지영 (인하대학교 의과대학 내과학교실) ;
  • 신용운 (인하대학교 의과대학 내과학교실) ;
  • 김영수 (인하대학교 의과대학 내과학교실)
  • Published : 2011.05.01

Abstract

Solid pseudopapillary tumors are rare primary neoplasms of the pancreas that have a relatively favorable prognosis, with a lowmalignant potential. Most patients present with non-specific clinical features, such as vague abdominal discomfort and a palpableabdominal mass. A 50-year-old woman who presented with hematemesis had an incidental pancreatic cystic mass on abdominalcomputed tomography (CT). We performed several tests, including upper endoscopy and angiography, but we could not find thebleeding focus. Therefore, we performed a pancreaticoduodenectomy. At laparotomy, there was a 10-cm encapsulated pancreaticmass with duodenal invasion, which showed a bleeding ulcer. A solid pseudopapillary tumor was diagnosed pathologically. Wereport a solid pseudopapillary tumor that presented with gastrointestinal bleeding.

고형 가유두상 종양은 췌장에 발생하는 저등급의 악성종양으로 주로 모호한 복통이나 복부덩어리를 주소로 내원하다. 대부분 우연히 발견하는데 저자들은 위장관 출혈로 내원한 환자에서 위내시경 등 여러 검사를 했으나, 정확한 출혈 병소를 찾지 못하였다. 우연히 췌장에 고형 가유두상 종양을 발견하여 절제하였고, 십이지장에 종양이 침범하여 형성된 궤양출혈을 확인하였다. 저자들은 토혈을 주소로 내원한고형 가유두상 종양 1예를 경험하였기에 문헌고찰과 함께 보고한다.

Keywords

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