Journal of Cardiovascular Imaging

Korean Society of Echocardiography (한국심초음파학회)
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CARCINOID HEART DISEASE: A RARE CAUSE OF RIGHT VENTRICULAR DYSFUNCTION EVALUATION BY TRANSTHORACIC 2D, DOPPLER AND 3-D ECHOCARDIOGRAPHY

  • Published : 2011.06.27
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Abstract

Carcinoid heart disease is a rare cause of heart failure with or without right valvular heart impairments. In this study, we showed a case of carcinoid tumour with hepatic metastases inducing carcinoid heart disease. Neuroendocrine heart involvement happens for severe tricuspid valve insufficiency and plaques on right ventricular (RV) walls produced by a release of serotonin (5-HT). A patient affected by primitive ileal tumour with 5-HT-secernent hepatic metastases inducing tricuspid insufficiency is showed. Transthoracic 2-D echocardiography showed tricuspid valve regurgitation and both right atrium, RV-walls plaques and RV dilation. Continue-wave Doppler showed a characteristic "dagger shaped" spectrum of tricuspid systolic flow. RV function was evaluated with 3-D transthoracic echocardiography. In particular, RV volumes, RV ejection fraction and stroke volume were defined by this technique. 2, 3-D echocardiography and Doppler method are useful techniques to show heart valves' derangements and RV function to non-invasively detect RV impairments in carcinoid heart disease.

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References

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  1. Current Concepts in Diagnosis and Perioperative Management of Carcinoid Heart Disease vol.17, pp.3, 2011, https://doi.org/10.1177/1089253212465475
  2. Isolated metastasis of mediastinal carcinoid to the left ventricle: A case report vol.38, pp.12, 2011, https://doi.org/10.1111/echo.15253