Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Epithelioid Hemangioendothelioma of the Femur with Benign Cystic Appearance

낭성 종괴의 자기공명영상 소견을 보인 대퇴골의 상피양혈관내피세포종

  • Kim, Yeo-Goon (Department of Radiology and Institute of Radiation Medicine, Seoul National University College of Medicine) ;
  • Choi, Jung-Ah (Department of Radiology, Seoul National University Bundang Hospital) ;
  • Chung, Jin-Haeng (Department of Pathology, Seoul National University Bundang Hospital) ;
  • Oh, Joo-Han (Department of Orthopedic Surgery, Seoul National University Bundang Hospital) ;
  • Kang, Heung-Sik (Department of Radiology, Seoul National University Bundang Hospital)
  • 김여군 (서울대학교 의과대학 영상의학과학교실) ;
  • 최정아 (분당서울대학교병원 영상의학과) ;
  • 정진행 (분당서울대학교병원 병리과) ;
  • 오주한 (분당서울대학교병원 정형외과) ;
  • 강흥식 (분당서울대학교병원 영상의학과)
  • Published : 2011.12.01
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Abstract

An epithelioid hemangioendothelioma is an intermediate grade tumor between hemangioma and angiosarcoma that frequently shows marked enhancement because it is a vascular tumor. Herein, we describe a rare case of a malignant epithelioid hemangioendothelioma of the femur that was mistaken as a benign lesion such as a simple bone cyst or fibrous dysplasia because the tumor had a benign cystic appearance on MRI and its imaging findings showed a histopathologic correlation.

상피양혈관내피세포종은 혈관종과 혈관육종 사이의 중증도 악성종양으로, 혈관성 종양이므로 균질하고 분명한 조영증강을 보이는 것으로 알려져 있다. 저자들은 대퇴골에 발생한 혈관내피세포종이 MR에서 낭성 종괴로 보여 양성종양과의 감별이 어려웠던 증례를 경험하여 이 증례의 영상 소견과 병리 소견을 비교하여 보고하고자 한다.

Keywords

References

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