Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Neurocutaneous Melanosis: A Case Report

신경피부흑색증: 증례 보고

  • Seo, Yoon-Nae (Department of Radiology, Busan Paik Hospital, Inje University College of Medicine) ;
  • Jeong, Hae-Woong (Department of Radiology, Busan Paik Hospital, Inje University College of Medicine) ;
  • In, Hyun-Sin (Department of Radiology, Busan Paik Hospital, Inje University College of Medicine)
  • 서윤내 (인제대학교 의과대학 부산백병원 영상의학과학교실) ;
  • 정해웅 (인제대학교 의과대학 부산백병원 영상의학과학교실) ;
  • 인현신 (인제대학교 의과대학 부산백병원 영상의학과학교실)
  • Published : 2011.12.01
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Abstract

Neurocutaneous melanosis is a rare disorder characterized by the presence of a large or multiple congenital melanocytic nevus with proliferation of melanocytes in the central nervous system. The prognosis of neurocutaneous melanosis is extremely poor and its diagnostic approach requires understanding its brain magnetic resonance imaging findings. We report a patient with asymptomatic neurocutaneous melanosis and its radiologic findings.

신경피부흑색증(neurocutaneous melanosis)은 여러 개 혹은 크기가 큰 선천성 멜라닌세포모반(congenital melanocytic nevus)과 중추신경계에 멜라닌세포의 증식을 특징으로 하는 신경피부증후군(neurocutaneous syndrome)이다. 신경피부흑색증은 드물게 발생하지만 예후가 나쁘기 때문에 진단적 접근을 위한 자기공명영상(MRI) 소견에 대한 이해가 필요하다. 이에 본 저자들은 영상학적 소견을 중심으로 신경피부흑색증 1예를 보고하고자 한다.

Keywords

References

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