Neonatal Medicine

The Korean Society of Neonatology (대한신생아학회)
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A Case of Acrodermatitis Enteropathica with Normal Serum Zinc Level in a Breastfed Preterm Infant

혈중 아연 농도가 정상인 모유수유를 한 미숙아에서 보인 장병성 선단 피부염 1례

  • Baek, Jung-Hyun (Department of Pediatrics, College of Medicine, Korea University) ;
  • Park, Chul (Department of Pediatrics, College of Medicine, Korea University) ;
  • Park, Kyu-Hee (Department of Pediatrics, College of Medicine, Korea University) ;
  • Lee, Jung-Hwa (Department of Pediatrics, College of Medicine, Korea University) ;
  • Hong, Young-Sook (Department of Pediatrics, College of Medicine, Korea University) ;
  • Lee, Joo-Won (Department of Pediatrics, College of Medicine, Korea University) ;
  • Baek, Yoo-Sang (Department of Dermatology, College of Medicine, Korea University) ;
  • Song, Hae-Jun (Department of Dermatology, College of Medicine, Korea University) ;
  • Lee, Jang-Hoon (Department of Pediatrics, Ajou University School of Medicine)
  • 백정현 (고려대학교 의과대학 소아청소년과학교실) ;
  • 박철 (고려대학교 의과대학 소아청소년과학교실) ;
  • 박규희 (고려대학교 의과대학 소아청소년과학교실) ;
  • 이정화 (고려대학교 의과대학 소아청소년과학교실) ;
  • 홍영숙 (고려대학교 의과대학 소아청소년과학교실) ;
  • 이주원 (고려대학교 의과대학 소아청소년과학교실) ;
  • 백유상 (고려대학교 의과대학 피부과학교실) ;
  • 송해준 (고려대학교 의과대학 피부과학교실) ;
  • 이장훈 (아주대학교 의과대학 소아과학교실)
  • Published : 2011.11.30
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Abstract

Acrodermatitis enteropathica due to zinc deficiency is characterized by periorificial dermatitis, alopecia, and intractable diarrhea. Here we report a case of transient acrodermatitis enteropathica in a 2-month-old preterm infant, whose skin is erythematous, scaly, eczematous, with an eruption starting from the periorificial area. While her serum zinc level was normal at 118.2 ug/dL, the serum alkaline phosphatase level was low at 48 IU/L and the serum alkaline phosphatase level get increased concordant with clinical improvement after zinc supplementation. Hence, this case shows that the diagnosis of zinc deficiency can be aided with a low level of serum alkaline phoaphatase although serum zinc level is normal.

Keywords

References

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