Clinical Endoscopy

The Korean Society of Gastrointestinal Endoscopy (대한소화기내시경학회)
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A Case of Chronic Neuropathic Pseudo-obstruction of the Colon

신경병증형 만성 대장 가성장폐색 1예

  • Kim, Sun-Yong (Department of Internal Medicine, Gang Dong Kyung Hee University Hospital, Kyung Hee University College of Medicine) ;
  • Kim, Min-Kyung (Department of Internal Medicine, Gang Dong Kyung Hee University Hospital, Kyung Hee University College of Medicine) ;
  • Jo, Uk (Department of Internal Medicine, Gang Dong Kyung Hee University Hospital, Kyung Hee University College of Medicine) ;
  • Chae, Jung-Min (Department of Internal Medicine, Gang Dong Kyung Hee University Hospital, Kyung Hee University College of Medicine) ;
  • Cha, Jae-Myung (Department of Internal Medicine, Gang Dong Kyung Hee University Hospital, Kyung Hee University College of Medicine) ;
  • Shin, A-Ri (Department of Internal Medicine, Gang Dong Kyung Hee University Hospital, Kyung Hee University College of Medicine) ;
  • Lim, Sung-Jig (Department of Internal Pathology, Gang Dong Kyung Hee University Hospital, Kyung Hee University College of Medicine) ;
  • Moon, Ah-Rim (Department of Internal Pathology, Gang Dong Kyung Hee University Hospital, Kyung Hee University College of Medicine)
  • 김선용 (경희대학교 의과대학 강동경희대학교병원 내과학교실) ;
  • 김민경 (경희대학교 의과대학 강동경희대학교병원 내과학교실) ;
  • 조욱 (경희대학교 의과대학 강동경희대학교병원 내과학교실) ;
  • 채정민 (경희대학교 의과대학 강동경희대학교병원 내과학교실) ;
  • 차재명 (경희대학교 의과대학 강동경희대학교병원 내과학교실) ;
  • 신아리 (경희대학교 의과대학 강동경희대학교병원 내과학교실) ;
  • 임성직 (경희대학교 의과대학 강동경희대학교병원 병리학교실) ;
  • 문아림 (경희대학교 의과대학 강동경희대학교병원 병리학교실)
  • Published : 2011.03.30
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Abstract

Colonic pseudo-obstruction, which is characterized by repetitive episodes or continuous symptoms and signs of a bowel obstruction, is a rare disease that results in colorectal dilatation without any obstructing lesions. Cases with neuropathic chronic colonic pseudo-obstruction have rarely been reported in Korea. We report a case of neuropathic colonic pseudo-obstruction, which results in decreased number of interstitial cells of Cajal and hypoganglionosis, in a 50-year-old man with chronic constipation accompanied by megacolon.

장폐쇄 증상과 징후가 반복적 또는 지속적으로 나타나는 것을 특징으로 하는 만성 가성 장폐쇄는 장관 내강의 해부학적인 폐쇄 부위가 없이 결장이 확장되는 드문 질환이다. 국내에서 신경병증형 만성 대장 가성 장폐쇄를 조직학적으로 확진한 증례는 매우 드물게 보고되었다. 저자들은 만성 변비를 호소하는 50세 남성에서 수술 후 병리 소견에서 Cajal 간질세포의 감소와 신경절 세포 감소증이 관찰되어, 신경병증형에 의한 만성 대장 가성 장폐쇄를 조직학적으로 진단한 증례를 보고한다.

Keywords

References

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