The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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Concurrent Thin Basement Membrane Disease and Minimal Change Disease: A Case Report

최소변화콩팥병증 환자에 동반된 얇은기저막병 1예

  • Seo, Jae-Won (Department of Internal Medicine, Seoul Veterans Hospital) ;
  • Lim, Byung-Hoon (Department of Internal Medicine, Seoul Veterans Hospital) ;
  • Lee, Hyun-Jeong (Department of Internal Medicine, Seoul Veterans Hospital) ;
  • Kang, Eun-Mi (Department of Internal Medicine, Seoul Veterans Hospital) ;
  • Lee, Byung-Uk (Department of Internal Medicine, Seoul Veterans Hospital) ;
  • Kim, Beom (Department of Internal Medicine, Seoul Veterans Hospital) ;
  • Cho, Yong-Mee (Department of Pathology, Asan Medical Center, University of Ulsan College of Medicine)
  • 서재원 (서울보훈병원 신장내과) ;
  • 임병훈 (서울보훈병원 신장내과) ;
  • 이현정 (서울보훈병원 신장내과) ;
  • 강은미 (서울보훈병원 신장내과) ;
  • 이병욱 (서울보훈병원 신장내과) ;
  • 김범 (서울보훈병원 신장내과) ;
  • 조영미 (울산대학교 의과대학 서울아산병원 병리과)
  • Published : 2011.04.01
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Abstract

Thin basement membrane disease is defined as diffuse thinning of the glomerular basement membrane, and is clinically characterized by persistent hematuria, minimal proteinuria, normal renal function, and a benign course. It can occur together with other glomerular diseases. We experienced a case of thin basement membrane disease concurrent with minimal-change disease. Treatment with corticosteroid resulted in improved proteinuria and peripheral edema during the follow-up period.

저자들은 최소변화콩팥병증에 동반된 얇은기저막병 증례를 경험하였으며, 통상적인 고용량 스테로이드 치료에 좋은 반응을 보였다. 향후 우리나라 성인에 있어서 얇은기저막병이 동반된 최소변화콩팥병증의 임상상에 대한 자료 수집과 분석이 필요할 것으로 생각된다.

Keywords

References

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