출혈이 동반된 점막하 종양 형태로 나타난 췌장 고형 가유두상 종양 1예

A Case of Solid Pseudopapillary Tumor of the Pancreas Presenting as a Submucosal Tumor with Hemorrhage

  • 김종한 (인제대학교 의과대학 부산백병원 내과학교실) ;
  • 이상헌 (인제대학교 의과대학 부산백병원 내과학교실) ;
  • 김지현 (인제대학교 의과대학 부산백병원 내과학교실) ;
  • 최병진 (인제대학교 의과대학 부산백병원 내과학교실) ;
  • 송영진 (인제대학교 의과대학 부산백병원 내과학교실) ;
  • 최상분 (인제대학교 의과대학 부산백병원 내과학교실) ;
  • 이재익 (인제대학교 의과대학 부산백병원 내과학교실) ;
  • 정수진 (인제대학교 의과대학 부산백병원 병리학교실)
  • Kim, Jong-Han (Department of Internal Medicine, Pusan Paik Hospital, Inje University College of Medicine) ;
  • Lee, Sang-Heon (Department of Internal Medicine, Pusan Paik Hospital, Inje University College of Medicine) ;
  • Kim, Ji-Hyun (Department of Internal Medicine, Pusan Paik Hospital, Inje University College of Medicine) ;
  • Choi, Byoung-Jin (Department of Internal Medicine, Pusan Paik Hospital, Inje University College of Medicine) ;
  • Song, Young-Jin (Department of Internal Medicine, Pusan Paik Hospital, Inje University College of Medicine) ;
  • Choi, Sang-Bun (Department of Internal Medicine, Pusan Paik Hospital, Inje University College of Medicine) ;
  • Lee, Jae-Ik (Department of Internal Medicine, Pusan Paik Hospital, Inje University College of Medicine) ;
  • Jung, Su-Jin (Department of Pathology, Pusan Paik Hospital, Inje University College of Medicine)
  • 발행 : 2011.06.30

초록

췌장의 고형성 가성유두상 종양은 드물게 보고되는 희귀 질환으로 전형적으로 젊은 여자에서 발생한다. 12세 여아가 빈혈을 주소로 내원하였다. 영상의학적 검사와 상부 위장관 내시경에서 췌장 두부에서 기원하는 것으로 보이는 7${\times}$4.5 cm 크기의 종양이 관찰되어 근치 절제술인 췌십이지장절제술을 시행하였고 조직검사에서 췌장의 고형 가유두상 종양으로 진단되어 문헌 고찰과 함께 보고한다.

A solid pseudopapillary tumor is a rare pancreatic tumor with a low malignant potential that occurs commonly in young females. We report a case of 12-year-old girl with a solid pseudopapillary tumor of the pancreas associated with symptoms of anemia. She was suspected to have a 7${\times}$4.5 cm mass growing from the head of the pancreas based on an esophagogastroduodenoscopy, a radiological imaging study, and an immunohistochemical stain examination. She was finally diagnosed with a solid pseudopapillary tumor after a pancreaticoduodenectomy as the definitive treatment.

키워드

참고문헌

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