Clinical Endoscopy

The Korean Society of Gastrointestinal Endoscopy (대한소화기내시경학회)
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A Case of Malignant Intraductal Papillary Mucinous Neoplasm of the Pancreas with Duodenal Adenocarcinoma

십이지장 샘암종과 동반된 악성 췌관 내 유두상 점액 종양 1예

  • Park, Kyoung-Suk (Departments of Internal Medicine, College of Medicine, Kwandong University) ;
  • Cho, Jae-Hee (Departments of Internal Medicine, College of Medicine, Kwandong University) ;
  • Park, Tae-Woon (Departments of Internal Medicine, College of Medicine, Kwandong University) ;
  • Ko, Geun-Jun (Departments of Internal Medicine, College of Medicine, Kwandong University) ;
  • Woo, Myoung-Lyeol (Departments of Internal Medicine, College of Medicine, Kwandong University) ;
  • Jeong, Jin-Ho (Department of Surgery, College of Medicine, Kwandong University) ;
  • Oh, Hwa-Eun (Department of Pathology, College of Medicine, Kwandong University)
  • 박경석 (관동대학교 의과대학 내과학교실) ;
  • 조재희 (관동대학교 의과대학 내과학교실) ;
  • 박태운 (관동대학교 의과대학 내과학교실) ;
  • 고근준 (관동대학교 의과대학 내과학교실) ;
  • 우명렬 (관동대학교 의과대학 내과학교실) ;
  • 정진호 (관동대학교 의과대학 외과학교실) ;
  • 오화은 (관동대학교 의과대학 병리학교실)
  • Published : 2011.04.30
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Abstract

Intraductal papillary mucinous neoplasm of the pancreas (IPMN) is a precancerous lesion with a well-described adenocarcinoma sequence. The rate of progression of IPMN appears to be very slow; however, patients with IPMN may be at increased risk for extrapancreatic malignancies. A 55-year-old female was diagnosed with IPMN of the pancreas and a duodenal polyp in 2004. After an approximate 3 year loss to follow-up, she was readmitted for managing abdominal pain and underwent Whipple's operation. Herein, we report a case of a patient with malignant IPMN accompanied by duodenal adenocarcinoma arising from a duodenal polyp.

췌관내 유두상 종양은 샘종에서 샘암종으로 분화하는 전암성병변이나 그 진행이 매우 느리다. 췌관내 유두상 종양 환자에서 췌장 외 악성 신생물의 발생 빈도가 증가되는 특징은 환 자의 예후에 있어서 매우 중요하다. 십이지장의 악성 신생물은 그 자체로도 드문 경우이며 췌관내 유두상 종양과 동반된 췌장외 악성 신생물이 십이지장에서 보고된 경우는 흔치 않기 때문에 저자들은 악성 IPMN과 동반된 십이지장 샘암종을 수술을 통해 치료하였고 18개월째 추적 관찰중인 증례를 문헌 고찰과 함께 보고한다.

Keywords

References

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