Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Symmetric Presentation of Melorheostosis Involving Multiple Flat Bones in the Thorax: A Case Report

흉곽에서 대칭적으로 편평골을 침범한 다발성 유선상과골증: 1예 보고

  • Oh, Jung-Suk (Department of Diagnostic Radiology, St. Vincent's Hospital, The Catholic University of Korea) ;
  • Park, Hyun-Jin (Department of Diagnostic Radiology, St. Vincent's Hospital, The Catholic University of Korea) ;
  • Kim, Jee-Young (Department of Diagnostic Radiology, St. Vincent's Hospital, The Catholic University of Korea) ;
  • Kim, Ki-Jun (Department of Diagnostic Radiology, Incheon St. Mary's Hospital, The Catholic University of Korea) ;
  • Jung, Won-Sang (Department of Diagnostic Radiology, St. Vincent's Hospital, The Catholic University of Korea)
  • 오정석 (가톨릭의대 성빈센트병원 영상의학과) ;
  • 박현진 (가톨릭의대 성빈센트병원 영상의학과) ;
  • 김지영 (가톨릭의대 성빈센트병원 영상의학과) ;
  • 김기준 (가톨릭의대 인천성모병원 영상의학과) ;
  • 정원상 (가톨릭의대 성빈센트병원 영상의학과)
  • Received : 2009.12.15
  • Accepted : 2010.04.20
  • Published : 2010.08.01
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Abstract

Melorheostosis is a rare bone dysplasia of unknown etiology that usually affects a single limb and is characterized by cortical thickening, with a flowing candle wax appearance, extending vertically along the surface of the long bone. We report a case of polyostotic melorheostosis symmetrically involving multiple flat bones, ribs, and the scapulas. This is the first case of melorheostosis symmetrically involving multiple flat bones.

유선상과골증은 원인 미상의 드문 골 이형성증이다. 대개 단일 사지를 침범하며, 장골의 표면을 따라 수직적으로 흐르는 촛농 모양의 피질비대가 특징적이다. 저자들은 다골성 유선상과골증이 늑골과 견갑골과 같은 편평골을 대칭적이고 다발성으로 침범한 예를 보고하고자 한다.

Keywords

References

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