Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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CT and MRI Findings of Angiomyolipoma with Epithelial Cysts of the Kidney: A Case Report

신장의 낭성 혈관근지방종의 CT와 MRI 영상 소견: 1예 보고

  • Yeo, Dong-Myung (Department of Radiology, St. Mary's Hospital, The Catholic University of Korea) ;
  • Chung, Dong-Jin (Department of Radiology, St. Mary's Hospital, The Catholic University of Korea) ;
  • Kim, Tae-Jung (Department of Pathology, St. Mary's Hospital, The Catholic University of Korea) ;
  • Lee, In-Kyu (Department of Surgery, St. Mary's Hospital, The Catholic University of Korea) ;
  • Hahn, Seong-Tai (Department of Radiology, St. Mary's Hospital, The Catholic University of Korea) ;
  • Lee, Jae-Mun (Department of Radiology, St. Mary's Hospital, The Catholic University of Korea)
  • 여동명 (가톨릭대학교 성모병원 영상의학과) ;
  • 정동진 (가톨릭대학교 성모병원 영상의학과) ;
  • 김태정 (가톨릭대학교 성모병원 병리과) ;
  • 이인규 (가톨릭대학교 성모병원 외과) ;
  • 한성태 (가톨릭대학교 성모병원 영상의학과) ;
  • 이재문 (가톨릭대학교 성모병원 영상의학과)
  • Received : 2010.01.13
  • Accepted : 2010.05.24
  • Published : 2010.08.01
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Abstract

Angiomyolipoma with epithelial cysts (AMLEC) or cystic angiomyolipoma has been recently described as a distinct cystic variant of angiomyolipoma. Although angiomyolipoma (AML) is usually composed of adipose, vascular, and muscular tissue lacking an epithelial element, AMLEC contains an epithelial component in the form of gross or microscopic cysts. To date, the radiologic appearance of AMLEC has been demonstrated in only one case report, as a solid mass containing a tiny cystic focus. This report shows another imaging feature of AMLEC, which presents as a multiloculated cystic mass without a visible solid portion on CT and MRI.

낭성 혈관근지방종은 혈관근지방종의 독특한 낭성 변종으로 최근에 알려졌다. 혈관근지방종은 지방, 혈관, 근조직으로 이루어져 상피조직을 포함하지 않는 것으로 알려져 있으나, 낭성혈관근지방종은 상피 조직을 거시적 혹은 미시적 낭종의 형태로 포함한다. 지금까지 영상소견에 대해 1예의 증례보고가 있었으며 작은 낭종을 포함하는 고형 종괴로 발현한 경우였다. 이 증례는 CT와 MRI에서 고형 성분은 보이지 않고 다방성 낭성 종괴로 발현한 예이다.

Keywords

References

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