Korean Journal of Radiology

  • 제11권1호
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  • Pages.119-122
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  • 2010
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  • 1229-6929(pISSN)
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  • 2005-8330(eISSN)
대한영상의학회 (The Korean Society of Radiology)
권호 표지
DOI QR코드

DOI QR Code

Prenatal Diagnosis of Bilateral Pulmonary Agenesis: a Case Report

  • Lee, Kyung-A (Department of Obstetrics and Gynecology, Seoul National University College of Medicine) ;
  • Cho, Jeong-Yeon (Department of Radiology and Institute of Radiation Medicine, Seoul National University College of Medicine) ;
  • Lee, Seung-Mi (Department of Obstetrics and Gynecology, Seoul National University College of Medicine) ;
  • Jun, Jong-Kwan (Department of Obstetrics and Gynecology, Seoul National University College of Medicine) ;
  • Kang, Jieun (Department of Pathology, Seoul National University College of Medicine) ;
  • Seo, Jeong-Wook (Department of Pathology, Seoul National University College of Medicine)
  • 투고 : 2009.05.19
  • 심사 : 2009.07.08
  • 발행 : 2010.02.01
⟨ 이전 논문 다음 논문 ⟩

초록

We report a case of bilateral pulmonary agenesis (BPA), which was suspected during a prenatal US examination and diagnosed by fetal magnetic resonance imaging (MRI). BPA is an extremely rare congenital anomaly and, although many fetal structural defects can be detected with a high degree of confidence after introducing high-resolution US, the prenatal diagnosis of BPA remains problematic. Other thoracic abnormalities, such as a congenital diaphragmatic hernia, congenital cystic adenomatoid malformation, and pulmonary sequestration, should be excluded from the list of possible diagnoses before coming to the conclusion of BPA, because BPA is absolutely incompatible with extrauterine life, and an accurate internal diagnosis can prevent a futile intervention from being performed.

키워드

참고문헌

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피인용 문헌

  1. Recurrent prenatally diagnosed isolated bilateral pulmonary agenesis vol.40, pp.6, 2012, https://doi.org/10.1002/uog.11146
  2. Usefulness of ultrasonography and MRI for diagnosis of fetal pulmonary agenesis: case report and review of the literature vol.40, pp.2, 2013, https://doi.org/10.1007/s10396-012-0410-7
  3. Bilateral Pulmonary Agenesis: A Rare and Unexpected Finding in a Newborn vol.6, pp.2, 2010, https://doi.org/10.1055/s-0036-1584530