Clinical Endoscopy

  • 제41권2호
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  • Pages.113-117
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  • 2010
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  • 2234-2400(pISSN)
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  • 2234-2443(eISSN)
대한소화기내시경학회 (The Korean Society of Gastrointestinal Endoscopy)
권호 표지

소장에 국한된 결절성 다발성 동맥염 1예

Polyarteritis Nodosa Localized in Small Intestine: A Case Report

  • 임병훈 (서울보훈병원 소화기내과) ;
  • 장지선 (서울보훈병원 소화기내과) ;
  • 김정원 (한림대학교 의과대학 강남성심병원 병리학교실) ;
  • 장세진 (울산대학교 의과대학 서울아산병원 병리학교실) ;
  • 김성훈 (서울보훈병원 소화기내과) ;
  • 방제소 (서울보훈병원 소화기내과) ;
  • 양수현 (서울보훈병원 소화기내과) ;
  • 변종훈 (서울보훈병원 소화기내과)
  • Lim, Byung-Hoon (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Jang, Ji-Sun (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Kim, Jung-Won (Hallym University Medical Center, Hallym University College of Medicine) ;
  • Jang, Se-Jin (Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Sung-Hoon (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Bang, Jei-So (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Yang, Soo-Hyun (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology) ;
  • Byun, Jong-Hoon (Department of Internal Medicine, Seoul Veterans Hospital, Department of Pathology)
  • 투고 : 2010.04.08
  • 심사 : 2010.07.08
  • 발행 : 2010.08.30
⟨ 이전 논문 다음 논문 ⟩

초록

일반적으로 혈관염은 다발성 장기를 침범하나, 단일 장기에 발생한 국소성 혈관염이 종종 보고되었다. 그러나 소화관에 국한되어 발생한 혈관염은 매우 드물며, 소장에 발생한 국소성 혈관염은 국내에서 보고된 바 없다. 저자들은 최근 반복되는 심한 장출혈이 있어 소장 절제 수술을 시행하고 수술 후 조직 검사에서 결절성 다발성 동맥염을 진단한 증례를 경험하였다. 환자는 혈관염을 의심할 만한 전신 증상 및 다른 장기를 침범하는 검사 소견이 없어 소장에 국한된 괴사성 혈관염으로 진단하였다.

Polyarteritis nodosa is a systemic necrotizing vasculitis that affects mainly small and medium-sized arteries that involve multiple organs. In addition to the systemic involvement of classical vasculitis, localized vasculitis involves blood vessels within a confined vascular distribution or single organ without clinical evidence of generalized inflammation. Localized vasculitis of the gastrointestinal tract is a rare entity. In particular, a limited involvement of the small bowel is an unusual manifestation of polyarteritis nodosa. In this report, we describe a case of biopsy-proven polyarteritis nodosa presenting as small bowel bleeding without other systemic manifestations.

키워드

참고문헌

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