The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
권호 표지

A case of angiomyolipoma of the liver

생검으로 진단된 간의 혈관근지방종 1예

  • Jang, Sung-Ill (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Park, Hyung-Soon (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Yu, Jung-Whan (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Bae, Sung-Chang (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Chung, Jae-Jun (Department of Radiology, Yonsei University College of Medicine) ;
  • Paik, Yong-Han (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Kim, Ja-Kyung (Department of Internal Medicine, Yonsei University College of Medicine)
  • 장성일 (연세대학교 의과대학 내과학교실) ;
  • 박형순 (연세대학교 의과대학 내과학교실) ;
  • 유정환 (연세대학교 의과대학 내과학교실) ;
  • 배성창 (연세대학교 의과대학 내과학교실) ;
  • 정재준 (연세대학교 의과대학 영상의학교실) ;
  • 백용한 (연세대학교 의과대학 내과학교실) ;
  • 김자경 (연세대학교 의과대학 내과학교실)
  • Received : 2009.07.31
  • Accepted : 2009.10.05
  • Published : 2010.09.01
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Abstract

Angiomyolipoma occurs most commonly in the kidneys; the liver is the second most frequent site of involvement. Hepatic angiomyolipoma is a rare, benign, mesenchymal neoplasm, composed mainly of blood vessels, smooth muscle cells, fat, and myelocomponents. Radiologic findings are non-specific because the various elements of these neoplasms vary in their proportion and distribution within the tumor. Thus, data obtained by imaging technologies such as computed tomography, ultrasonography, or magnetic resonance imaging tend to be merely suggestive; definitive diagnosis usually requires histologic confirmation. We report here a case of angiomyolipoma in an incidental tumor of the liver of a 53-year-old female. Tissue was removed from the tumor by ultrasonography-guided gun biopsy and subjected to immunohistochemical analysis. Data showed that tumor cells were positive for HMB-45 and SMA, but negative for cytokeratin, anti-hepatocyte antigen, and ${\alpha}$-fetoprotein. The patient did not receive any treatment and is being followed up.

저자들은 건강검진상 우연히 발견된 간내종물에 대해 생검을 시행하여 간의 혈관근지방종으로 진단된 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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