The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
권호 표지

A case of hyperglycemia-induced hemiballism-hemichorea associated with diabetic ketoacidosis

당뇨병성 케톤산증과 동반된 편무도증 1예

  • Kim, Hyun-Sung (Department of Internal Medicine, Hallym University College of Medicine) ;
  • Lee, Seo-Hee (Department of Internal Medicine, Hallym University College of Medicine) ;
  • Kang, Jun-Goo (Department of Internal Medicine, Hallym University College of Medicine) ;
  • Kim, Chul-Sik (Department of Internal Medicine, Hallym University College of Medicine) ;
  • Ihm, Sung-Hee (Department of Internal Medicine, Hallym University College of Medicine) ;
  • Yoo, Hyung-Joon (Department of Internal Medicine, Hallym University College of Medicine) ;
  • Lee, Seong-Jin (Department of Internal Medicine, Hallym University College of Medicine)
  • 김현성 (한림대학교 의과대학 내과학교실) ;
  • 이서희 (한림대학교 의과대학 내과학교실) ;
  • 강준구 (한림대학교 의과대학 내과학교실) ;
  • 김철식 (한림대학교 의과대학 내과학교실) ;
  • 임성희 (한림대학교 의과대학 내과학교실) ;
  • 유형준 (한림대학교 의과대학 내과학교실) ;
  • 이성진 (한림대학교 의과대학 내과학교실)
  • Received : 2009.06.13
  • Accepted : 2009.09.08
  • Published : 2010.07.01
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Abstract

Hemiballism-hemichorea (HB-HC) is defined as continuous, non-patterned, and involuntary movement involving one side of the body and is often associated with endocrine diseases such as diabetes mellitus (DM) and hyperthyroidism. In Korea, 16 cases of HB-HC associated with non-ketotic hyperglycemia have been reported. Here, we report the first known case of HB-HC associated with type 2 DM and diabetic ketoacidosis (DKA). A 32-year-old man visited our hospital complaining of hemichoreoballistic movement. The patient had no history of DM. In a neurological examination and laboratory tests, HB-HC associated with type 2 DM and DKA was diagnosed. The patient was immediately treated with intravenous hydration and insulin therapy, and completely recovered. DKA and non-ketotic hyperglycemia should be considered as a possible cause of HB-HC, although these are very rare. In HB-HC associated with DKA, strict blood glucose control is needed.

저자들은 당뇨병의 과거력이 없으면서 건강하게 지내던 중 제2형 당뇨병, 당뇨병성 케톤산증, 급성 신부전과 동반된 편무도증이 발병한 환자에서 충분한 수액공급과 인슐린 투여 등으로 집중 치료한 결과 편무도증이 소실된 증례를 국내에서 처음으로 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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