Journal of the Korean Association of Oral and Maxillofacial Surgeons

The Korean Association of Oral and Maxillofacial Surgeons (대한구강악안면외과학회)
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Mesenchymal chondrosarcoma on right mandible: a case report

우측 하악부에 발생한 간엽성 연골육종: 증례보고

  • Suh, Joon-Ho (Departments of Oral and Maxillofacial Surgery, School of Dentistry, Kyung Hee University) ;
  • Kim, Yeo-Gab (Departments of Oral and Maxillofacial Surgery, School of Dentistry, Kyung Hee University) ;
  • Kwon, Yong-Dae (Departments of Oral and Maxillofacial Surgery, School of Dentistry, Kyung Hee University) ;
  • Choi, Byung-Joon (Departments of Oral and Maxillofacial Surgery, School of Dentistry, Kyung Hee University) ;
  • Kim, Young-Ran (Departments of Oral and Maxillofacial Surgery, School of Dentistry, Kyung Hee University) ;
  • Lee, Baek-Soo (Departments of Oral and Maxillofacial Surgery, School of Dentistry, Kyung Hee University)
  • 서준호 (경희대학교 치과대학 구강악안면외과) ;
  • 김여갑 (경희대학교 치과대학 구강악안면외과) ;
  • 권용대 (경희대학교 치과대학 구강악안면외과) ;
  • 최병준 (경희대학교 치과대학 구강악안면외과) ;
  • 김영란 (경희대학교 치과대학 구강악안면외과) ;
  • 이백수 (경희대학교 치과대학 구강악안면외과)
  • Received : 2010.02.04
  • Accepted : 2010.03.30
  • Published : 2010.04.30
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Abstract

Mesenchymal chondrosarcoma is very aggressive and represents approximately 1% of all chondrosarcomas. While it affects a very wide age range, the peak frequency is in the second decade of life. It may occur in the head and rib region with a predilection for the maxillofacial skeleton. The small cell undifferentiated component may assume a hemangiopericytoma-like vascular pattern and should be distinguished from hemangiopericytoma. Treatment is en bloc resection, the intended tissue margins of excision should be designed to extend well beyond the actual tumor margin, as mesenchymal chondrosarcomas. Aggressive behavior of mesenchymal chondrosarcoma of the jaw, with a tendency for delayed recurrence and metastasis even many years after treatment. The most frequent site of metastasis was the lung. Here we present 52 years old, female case of mesenchymal chondrosarcoma occurs on Rt. mandible.

Keywords

References

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