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Myxofibrosarcoma of the Chest Wall

흉벽에 발생한 점액섬유육종

  • Kim, Myoung-Young (Department of Thoracic and Cardiovascular Surgery, Samsung Changwon Hospital, Sungkyunkwan University School of Medicine) ;
  • Kim, Han-Yong (Department of Thoracic and Cardiovascular Surgery, Samsung Changwon Hospital, Sungkyunkwan University School of Medicine) ;
  • Yoo, Byung-Ha (Department of Thoracic and Cardiovascular Surgery, Samsung Changwon Hospital, Sungkyunkwan University School of Medicine) ;
  • Hwang, Sang-Won (Department of Thoracic and Cardiovascular Surgery, Samsung Changwon Hospital, Sungkyunkwan University School of Medicine)
  • 김명영 (성균관대학교 의과대학 삼성창원병원 흉부외과학교실) ;
  • 김한용 (성균관대학교 의과대학 삼성창원병원 흉부외과학교실) ;
  • 유병하 (성균관대학교 의과대학 삼성창원병원 흉부외과학교실) ;
  • 황상원 (성균관대학교 의과대학 삼성창원병원 흉부외과학교실)
  • Received : 2010.06.06
  • Accepted : 2010.08.17
  • Published : 2010.12.05

Abstract

Myxofibrosarcoma is one of the most common soft tissue tumors in elderly patients, mostly arising in the extremities, and rarely arising in the chest wall. A 53-year-old women presented with a painful chest wall mass in the manubrium. We excised the mass. The mass was located subdermally, but had infiltrated the underlying muscle layer, and was histologically diagnosed as an intermediate grade myxofibrosarcoma showing myxoid changes and hypercellularity. Here we report a rare case of chest wall myxofibrosarcoma and present a review of the literature.

점액섬유육종은 장년의 환자에서 가장 흔한 연조직 종양중 하나로 주로 사지에서 발생하며, 흉벽에서는 드물게 발생한다. 53세 여자 환자가 흉골(manubrium)에 통증을 동반한 흉벽종괴를 주소로 내원하여, 종양적출술을 받았다. 종괴는 근육층까지 침범한 피하층 종양으로 조직검사상 점액성 변화와 세포의 고충실성을 보이는 중등급의 점액섬유육종으로 진단되었다. 드문 질환으로 알려진 흉벽의 점액섬유육종을 치험하였기에 문헌 고찰과 함께 보고하는 바이다.

Keywords

References

  1. Angervall L, Kindblom LG, Merck C. Myxofibrosarcoma. A study of 30 cases. Acta Pathol Microbiol Scand A 1977; 85A:127-40.
  2. Mentzel T, Calonje E, Wadden C, et al. Myxofibrosarcoma. Clinicopathologic analysis of 75 cases with emphasis on the low-grade variant. Am J Surg Pathol 1996;20:391-405.
  3. Mitsuhashi T, Barr RJ, Machtinger LA, et al. Primary cutaneous myxofibrosarcoma mimicking pleomorphic hyalinizing angiectatic tumor (PHAT): a potential diagnostic pitfall. Am J Dermatopathol 2005;27:322-6. https://doi.org/10.1097/01.dad.0000171605.48186.31
  4. Clarke LE, Zhang PJ, Crawford GH, et al. Myxofibrosarcoma in the skin. J Cutan Pathol 2008;35:935-40. https://doi.org/10.1111/j.1600-0560.2007.00922.x
  5. King RM, Pairolero PC, Trastek VF, Piehler JM, Payne WS, Bernatz PE. Primary chest wall tumors: factors affecting survival. Ann Thorac Surg 1986;41:597-601. https://doi.org/10.1016/S0003-4975(10)63067-6
  6. Yoshida N, Miyanari N, Yamamoto Y, et al. Successful treatment of malignant fibrous histiocytoma originating in the chest wall: report of a case. Surg Today 2006;36:714-21. https://doi.org/10.1007/s00595-004-3229-z
  7. Aoki T, Watanabe M, Takagi K, Tanaka S, Ogata T, Terahata S. Successful preoperative intra-arterial chemotherapy and concurrent radiotherapy for recurrent chest wall malignant fibrous histiocytoma. Nippon Kyobu Geka Gakkai Zasshi 1994;42:1117-22.
  8. Tsukushi S, Nishida Y, Sugiura H, et al. Soft tissue sarcomas of the chest wall. J Thorac Oncol 2009;4:834-7. https://doi.org/10.1097/JTO.0b013e3181a97da3