Dementia and Neurocognitive Disorders (대한치매학회지)

Korean Dementia Association (대한치매학회)
권호 표지

Focal Dystonia as an Initial Manifestation of Sporadic Creutzfeldt-Jakob Disease with Uncommon MRI Findings

  • Kim, Ji-Hoon (Department of Neurology, Konyang University College of Medicine) ;
  • Lee, Kee-Ook (Department of Neurology, Konyang University College of Medicine)
  • Published : 2010.09.30
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Abstract

Sporadic Creutzfeldt-Jakob disease (CJD) is a rare progressive spongiform encephalopathy. Involuntary movements commonly occur in the course of sporadic CJD, but focal dystonia alone as an initial manifestation is rare. We described a 40-yr-old man who presented with a 2 week history of focal dystonia in the neck and left arm. Interestingly, diffusion-weighted images revealed high signal intensities in the right temporal, posterior parietal, and occipital cortices rather than in the striatum.

Keywords

References

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