Archives of Plastic Surgery

Korean Society of Plastic and Reconstructive Surgeons (대한성형외과학회)
권호 표지

Correction of Frontal bone defect in Cleidocranial Dysostosis with Porous Polyethylene(Medpor®): A case report

쇄골두개이형성증(Cleidocranial Dysostosis)환자에서 Porous Polyethylene(Medpor®)를 이용한 두개골 함몰의 교정 1례

  • Moh, Jae Seong (Department of Plastic & Reconstructive Surgery, Wonkwang University Hospital) ;
  • Na, Young Cheon (Department of Plastic & Reconstructive Surgery, Wonkwang University Hospital)
  • 모재성 (원광대학교 성형외과학 교실) ;
  • 나영천 (원광대학교 성형외과학 교실)
  • Published : 2009.07.15
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Abstract

Purpose: Cleidocranial dysostosis is a rare hereditary disorder affecting bones that develop by intramembranous formation. The typical features include excessive growth of transverse diameter of the skull, hypoplastic clavicles, low height and characteristic facial features. Methods: A 28 years old female patient visited by frontal area depression. The diagnosis was performed by computed tomographic study and radiographic imaging. The patient has widely opened anterior fontanelle, partial fused metopic suture, multiple wormian bone and supernumenary impacted teeth. Under the coronal incision, we exposed depressed frontal area and corrected with Medpor block carving. Results: Postoperatively, frontoparietal skull was aestheticlly improved and she was satisfied with the results. Conclusion: Authors report a case of cleiodocranial dysostosis who has been done correction of abnormal skull shape by Medpor$^{(R)}$ insertion.

Keywords

Acknowledgement

Supported by : 원광대학교

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