Investigative Magnetic Resonance Imaging

Korean Society of Magnetic Resonance in Medicine (대한자기공명의과학회)
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Desmoplastic Fibroma of Distal Femur: A Case Report

결합조직형성 섬유종: 증례 보고

  • Song, Joon-Ho (Department of Diagnostic Radiology, University of Inje College of Medicine) ;
  • Shim, Jae-Chan (Department of Diagnostic Radiology, University of Inje College of Medicine) ;
  • Lee, Ghi-Jae (Department of Diagnostic Radiology, University of Inje College of Medicine) ;
  • Kim, Jin-Goo (Department of Orthopaedic Surgery, University of Inje College of Medicine, Seoul Paik Hospital) ;
  • Kang, Yun-Kyung (Department of Pathology, University of Inje College of Medicine, Seoul Paik Hospital)
  • 송준호 (인제대학교 의과대학 서울백병원 영상의학과) ;
  • 심재찬 (인제대학교 의과대학 서울백병원 영상의학과) ;
  • 이기재 (인제대학교 의과대학 서울백병원 영상의학과) ;
  • 김진구 (인제대학교 의과대학 서울백병원 정형외과) ;
  • 강윤경 (인제대학교 의과대학 서울백병원 병리과)
  • Published : 2009.12.30
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Abstract

Desmoplastic fibroma of bone is an extremely rare tumor that was first described by Jaffe in 1958. It histologically resembles the desmoid tumor of soft tissue. It is known as locally aggressive tumor but we experienced definitely benign and resembling simple bone cyst radiographically. We report a case of desmoplastic fibroma of bone and it should be included in the differential diagnosis list of any lytic bone lesion. The radiograph, MR imaging features, radiological and pathological differential diagnosis of the case are described, and literatures are reviewed.

결합조직형성 섬유종은 골에 발생하는 종양중 매우 드문종양으로 조직학적으로 연부조직에서 발생하는 유건종과 유사하다. 이 양성 종양은 국소적으로 주위 조직에 침윤성으로 성장한다. 방사선학적으로 고립성 골낭종, 섬유성 골이 형성증, 거대세포종, 골육종과 감별이 쉽지 않다. 저자들은 방사선학적으로 골낭종과 비슷한 형태를 보이는 원위 대퇴골에 생긴 결합조직형성 섬유종을 경험하고 드문 골 종양임으로 참고문헌과 함께 보고하는 바이다.

Keywords

References

  1. Dahlin DC. Unni KK. Bone Tumors. 3rd Ed. Springfield, Illinois: Thomas, 1978:325-326
  2. Gebhardt MC, Campbell CJ. Schiller AL, Mankin MJ. Desmoplastic fibroma of bone. A report of eight cases and review of the literature. J Bone Joint Surg Am 1985;67:732-747 https://doi.org/10.2106/00004623-198567050-00008
  3. Nishida J, Tajima K. Ahe M. Ilonda M, Inoniata Y, Shimanianiura T, et al. Desmoplastic fibroma. Aggressive curettage as a surgical alternative for treatment. Clin Orthop 1995:142-148
  4. Enneking WF. Musculoskeletal Tumor Surgery. New York, Churchill Livingstone, 1983:827-834
  5. Dorfman HD, Czerniak B. Bone tumors. St. Louis: Mosby, 1998:514-529
  6. Inwards JY, Unni KK, Beabout JW, Sim FH. Desmoplastic fibroma of bone. Cancer 1991;68:1978-1983 https://doi.org/10.1002/1097-0142(19911101)68:9<1978::AID-CNCR2820680922>3.0.CO;2-H
  7. Thirupathi RG, Vuletin JC, Wadwa R, Ballah S. Desmoplastic fibroma of the ulna. Clin Orthop 1983;179:231-238
  8. Vanhoenacker FM, Hauben E, De Beuckeleer LH, Willemen D, Van Marck E, DeSchepper AM. Desmoplastic fibroma of bone: MRI features. Skeletal Radiol 2000;29:171-175 https://doi.org/10.1007/s002560050589
  9. Sugiura I. Desmoplastic fibroma. Case report and review of the literature. J Bone Joint Surg Am 1976;58:126-130 https://doi.org/10.2106/00004623-197658010-00024
  10. Hertoni F. Bacchini P, Fahhri N, Mercuri M, Pic챠 P, Ruggieri P, et al. Osteosarcoma. Low-grade intraosseous type osteosarcoma,histologically resembling parosteal ostcosarconia, fibrous dysplasia and desmoplastic fibroma. Cancer 1993;71:338-345 https://doi.org/10.1002/1097-0142(19930115)71:2<338::AID-CNCR2820710212>3.0.CO;2-H