Generalized Lymphangiomatosis: A Case Report

전신성 림프관종증: 증례 보고

  • Cha, Jang-Gyu (Department of Radiology, Soonchunhyang University Bucheon Hospital) ;
  • Park, Jai-Soung (Department of Radiology, Soonchunhyang University Bucheon Hospital) ;
  • Paik, Sang-Hyun (Department of Radiology, Soonchunhyang University Bucheon Hospital) ;
  • Kim, Hee-Kyung (Department of Pathology, Soonchunhyang University Bucheon Hospital)
  • 차장규 (순천향대학교 부천병원 영상의학과) ;
  • 박재성 (순천향대학교 부천병원 영상의학과) ;
  • 백상현 (순천향대학교 부천병원 영상의학과) ;
  • 김희경 (순천향대학교 부천병원 병리학과)
  • Published : 2009.12.30

Abstract

Generalized lymphangiomatosis is a rare congenital malformation of the lymphatics. CT and MR scan have been used to evaluate lymphangiomas, which appear as large multicystic fluid-filled masses. CT and MR Imaging findings are often helpful in distinguishing lymphangiomas from various vascular disorders. We report the findings of CT, MRI and bone scan in a patient with generalized cystic lymphangiomatosis. Whole body 3.0-T MR scan using STIR sequence with a larger FOV could detect the additional lesions that were not seen at other imaging modalities. We believe that whole body 3.0 T MR imaging is a good modality to evaluate the extent of the disease and following up the patients with the generalized cystic lymphangiomatosis.

전신성 림프관종증은 림프관의 드문 선천성 기형이다. CT와 MR 영상은 림프관종 진단에 이용되고 있고 액체로 가득찬 다낭성의 큰 종괴로 보이고 이러한 영상 소견으로 림프관종과 다양한 혈관 질환을 감별하는 데 도움이 된다. 저자는 전신성 림프관종증 환자의 CT, MR영상과 방사선 동위원소 영상소견을 보고한다. STIR 영상 연쇄 기법을 이용한 전신 3.0-T MR 영상은 고해상도 다른 영상 장비에서 진단하지 못한 부가적인 병변을 발견할 수 있었다. 저자는 전신 3.0T MR 영상이 전신성 림프관종증 환자의 침범정도 평가나 추적관찰에 유용한 진단 장비라고 생각한다.

Keywords

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