Neonatal Medicine

The Korean Society of Neonatology (대한신생아학회)
권호 표지

A Case of Amniotic Band Syndrome Associated with Aplasia Cutis of the Scalp

두피 피부 무형성증을 동반한 양막대증후군 1례

  • Lee, Kyung-Yeon (Department of Pediatrics, University of Ulsan College of Medicine) ;
  • Kim, Ja-Hyeong (Department of Pediatrics, University of Ulsan College of Medicine) ;
  • Oh, Ki-Won (Department of Pediatrics, University of Ulsan College of Medicine) ;
  • Jeong, Jin-Young (Department of Pediatrics, University of Ulsan College of Medicine) ;
  • Park, Sang-Kyu (Department of Pediatrics, University of Ulsan College of Medicine) ;
  • Kim, Joon-Sung (Department of Pediatrics, University of Ulsan College of Medicine)
  • 이경연 (울산대학교 의과대학 소아과학교실) ;
  • 김자형 (울산대학교 의과대학 소아과학교실) ;
  • 오기원 (울산대학교 의과대학 소아과학교실) ;
  • 정진영 (울산대학교 의과대학 소아과학교실) ;
  • 박상규 (울산대학교 의과대학 소아과학교실) ;
  • 김준성 (울산대학교 의과대학 소아과학교실)
  • Published : 2009.05.31

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Abstract

The amniotic band syndrome is an uncommon congenital fetal abnormality, presumably due to fetal entanglement in strands of ruptured amniotic sac. The defects caused by this syndrome vary from simple limb defects to major visceral and craniofacial defects. We cared for a newborn infant with this syndrome, who showed constriction rings of the right leg and right axilla, right club foot, thoracic scoliosis, polydactyly, absence of the right thumb and aplasia cutis of the scalp. We report this case with a brief review of the literature.

저자들은 우측 다리와 겨드랑이의 협착고리, 우측 발의 만곡족, 척추 측만증, 좌측 엄지 손가락의 다지증, 우측 엄지 손가락 결여증과 더불어, 두피에 피부 무형성증이 동반된 양막대증후근 1례를 경험하였기에 문헌 괓ㄹ과 함께 보고하는 바이다.

Keywords

References

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