Spontaneous Massive Hemothorax Associated with Solitary Posterior Mediastinal Neurilemmoma

자발성 대량 혈흉이 발생한 단일 후종격동 신경집종

  • Kim, In Seon (Department of Internal Medicine, Ewha Womans University School of Medicine) ;
  • Lee, Jin Hwa (Department of Internal Medicine, Ewha Womans University School of Medicine) ;
  • Kim, Kwan Chang (Department of Thoracic Surgery, Ewha Womans University School of Medicine) ;
  • Kim, Yoo Ri (Department of Internal Medicine, Ewha Womans University School of Medicine) ;
  • Park, Jin Kyeong (Department of Internal Medicine, Ewha Womans University School of Medicine) ;
  • Lim, So Yeon (Department of Internal Medicine, Ewha Womans University School of Medicine) ;
  • Ryu, Yon Ju (Department of Internal Medicine, Ewha Womans University School of Medicine) ;
  • Chun, Eun Mi (Department of Internal Medicine, Ewha Womans University School of Medicine) ;
  • Chang, Jung Hyun (Department of Internal Medicine, Ewha Womans University School of Medicine) ;
  • Kim, Yoo Kyung (Department of Radiology, Ewha Womans University School of Medicine) ;
  • Shim, Sung Shin (Department of Radiology, Ewha Womans University School of Medicine) ;
  • Sung, Sun Hee (Department of Pathology, Ewha Womans University School of Medicine)
  • 김인선 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 이진화 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 김관창 (이화여자대학교 의학전문대학원 흉부외과학교실) ;
  • 김유리 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 박진경 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 임소연 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 류연주 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 천은미 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 장중현 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 김유경 (이화여자대학교 의학전문대학원 영상의학교실) ;
  • 심성신 (이화여자대학교 의학전문대학원 영상의학교실) ;
  • 성순희 (이화여자대학교 의학전문대학원 병리학교실)
  • Received : 2008.09.08
  • Accepted : 2008.09.17
  • Published : 2008.11.30

Abstract

Neurogenic tumors are common in posterior mediastinal tumors and neurilemmoma represents approximately 40% of neurogenic tumors arising in the mediastinum. It is usually asymptomatic, and is generally diagnosed incidentally. In some cases, they presented with symptoms of nerve or airway compression. However, a solitary neurilemmoma, particularly not associated with von Recklinghausen disease, with spontaneous hemothorax is quite rare. We report a case of spontaneous massive hemothorax associated with a solitary neurilemmoma.

신경종은 흔한 후종격동 종양으로, 신경집종은 종격동에 발생하는 신경종의 40%를 차지한다. 신경집종은 대개 무증상으로 우연히 발견된다. 일부 환자에서 종양이 신경이나 기도를 눌러서 증상이 나타날 수 있다. 그러나, 제1형 신경섬유종증이 아닌 단일 신경집종에 의한 자발성 혈흉은 매우 드물다. 저자들은 자발성 대량 혈흉을 동반한 단일 신경집종을 경험하여 보고한다.

Keywords

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