심인성 폐부종과 폐포성 출혈을 보인 갈색세포종 1예

A Case of Pheochromocytoma Accompanied with Alveolar Hemorrhage and Cardiogenic Pulmonary Edema

  • 정종필 (광주기독병원 내과) ;
  • 반희정 (전남대학교 의과대학 내과학교실) ;
  • 김수옥 (미래로 21병원 내과) ;
  • 손준광 (서남대학교 의과대학 내과학교실) ;
  • 주진영 (전남대학교 의과대학 내과학교실) ;
  • 권용수 (전남대학교 의과대학 내과학교실) ;
  • 오인재 (전남대학교 의과대학 내과학교실) ;
  • 김규식 (전남대학교 의과대학 내과학교실) ;
  • 김유일 (전남대학교 의과대학 내과학교실) ;
  • 임성철 (전남대학교 의과대학 내과학교실) ;
  • 김영철 (전남대학교 의과대학 내과학교실)
  • Jeong, Jong Pil (Department of Internal Medicine, Gwangju Christian Hospital) ;
  • Ban, Hee Jung (Department of Pulmonary and Critical Care Medicine, Chonnam National University Medical School) ;
  • Kim, Soo Ock (Department of Internal Medicine, Miraero21 Hospital) ;
  • Son, Jun Gwang (Department of Internal Medicine, Seonam University College of Medicine) ;
  • Ju, Jin Yung (Department of Pulmonary and Critical Care Medicine, Chonnam National University Medical School) ;
  • Kwon, Yong Soo (Department of Pulmonary and Critical Care Medicine, Chonnam National University Medical School) ;
  • Oh, In Jae (Department of Pulmonary and Critical Care Medicine, Chonnam National University Medical School) ;
  • Kim, Kyu Sik (Department of Pulmonary and Critical Care Medicine, Chonnam National University Medical School) ;
  • Kim, Yu Il (Department of Pulmonary and Critical Care Medicine, Chonnam National University Medical School) ;
  • Lim, Sung Chul (Department of Pulmonary and Critical Care Medicine, Chonnam National University Medical School) ;
  • Kim, Young Chul (Department of Pulmonary and Critical Care Medicine, Chonnam National University Medical School)
  • 투고 : 2008.01.05
  • 심사 : 2008.02.20
  • 발행 : 2008.03.30

초록

저자들은 대량 객혈로 내원한 환자에서 폐 출혈과 함께 반복적인 심인성 폐부종, 카테콜라민 유도성 심부전이 합병된 드문 형태의 갈색세포종을 경험하여 이러한 임상 증상시 폐나 심장 질환 외에 갈색세포종에 대한 고려가 필요할 것으로 생각되어 문헌고찰과 함께 보고하는 바이다.

Pheochromocytoma is derived from the chromaffin tissue. The typical finding of pheochromocytoma is paroxysmal hypertension accompanied with various signs and symptoms that are due to the excess of catecholamines or other bioactive substances. Yet the diagnosis is sometimes difficult to make because its clinical presentation is quite variable. Especially, hemoptysis is a very rare symptom, so the diagnosis is often missed or delayed. Without making the correct diagnosis and then subsequently administering treatment, the condition may be fatal. We herein report on a 68 year-old woman who was admitted because of abdominal pain and hemoptysis. The initial radiologic findings suggested pulmonary edema with alveolar hemorrhage. The urine catecholamine levels were elevated and she developed catecholamine-induced cardiomyopathy. We performed bronchial arterial embolization and we administered alpha blocker medication for controlling the hemoptysis and hypertension. After the temporary symptomatic improvement, her clinical course was aggravated by pneumonia and pulmonary edema. In spite of performing definitive surgery for pheochromocytoma, she died of postoperative hemodynamic instability.

키워드

참고문헌

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