The Journal of Korea Assosiation for Disability and Oral Health (대한장애인치과학회지)

Korean Association for Disability and Oral Health (대한장애인치과학회)
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MILD HEMOPHILIA A DETECTED BY DELAYED BLEEDING: A CASE REPORT

지연된 출혈로 밝혀진 경증 혈우병 A에 대한 증례 보고

  • Song, Je-Seon (Department of Oral and Maxillofacial Surgery, College of Dentistry and Oral Science Research Center, Yonsei University) ;
  • Choi, Byung-Jai (Department of Oral and Maxillofacial Surgery, College of Dentistry and Oral Science Research Center, Yonsei University) ;
  • Kim, Seong-Oh (Department of Oral and Maxillofacial Surgery, College of Dentistry and Oral Science Research Center, Yonsei University) ;
  • Lee, Jae-Ho (Department of Oral and Maxillofacial Surgery, College of Dentistry and Oral Science Research Center, Yonsei University) ;
  • Son, Heung-Gyu (Department of Pediatric Dentistry, College of Dentistry and Oral Science Research Center, Yonsei University) ;
  • Kim, Hyung-Jun (Department of Oral and Maxillofacial Surgery, College of Dentistry and Oral Science Research Center, Yonsei University) ;
  • Choi, Hyung-Jun (Department of Oral and Maxillofacial Surgery, College of Dentistry and Oral Science Research Center, Yonsei University)
  • 송제선 (연세대학교 치과대학 소아치과학교실, 구강과학연구소) ;
  • 최병재 (연세대학교 치과대학 소아치과학교실, 구강과학연구소) ;
  • 김성오 (연세대학교 치과대학 소아치과학교실, 구강과학연구소) ;
  • 이제호 (연세대학교 치과대학 소아치과학교실, 구강과학연구소) ;
  • 손흥규 (연세대학교 치과대학 소아치과학교실, 구강과학연구소) ;
  • 김형준 (연세대학교 치과대학 구강악안면외과학교실, 구강과학연구소) ;
  • 최형준 (연세대학교 치과대학 소아치과학교실, 구강과학연구소)
  • Published : 2008.12.31
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Abstract

Hemophilia A is an X-linked disorder resulting from a deficiency in factor VIII. Hemophilia A is classified into severe, moderate, and mild forms. A 12-month old boy visited for uncontrolled bleeding on the upper labial frenum area. Spontaneous bleeding occurred about 13 days ago. We sutured the wound. However, the patient returned after 6 days with large hematoma formation. Consultation to the hematologist and laboratory examination were carried out. Activated PTT was elongated and factor VIII was only 6%. He was diagnosed as mild hemophilia A. Fresh frozen plasma (FFP) was provided and hemostasis was achieved. At 5-day check-up, no more bleeding was observed. For the management of prolonged bleeding in hemophilia A patient, not only local hemostatic measures, but factor VIII replacement therapy, antifibrinolytics, and Desmopressin are also available. Mild hemophilia A often occurs without either familial or medical history. It is often first detected by dental trauma.

만 1세의 남아가 입에서 피가 계속 난다는 주소로 본과에 내원하였으며 지혈을 위해 봉합술을 시행하였다. 수일 후 다시 출혈 양상이 관찰되어 혈액종양과 협진 의뢰 및 임상 병리검사를 시행하여 경증의 혈우병 A 로 진단하였고 FFP를 투여하여 최종 지혈을 얻었다. 경증의 혈우병은 치과 외상을 통해 처음 발견되는 경우가 종종 있기 때문에 출혈이 지속되거나 수일 후 재발되는 경우에는 혈액 관련 전문가에게 의뢰하고 병리 검사를 시행하는 것이 바람직하다.

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