Imaging Science in Dentistry
- Volume 38 Issue 2
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- Pages.109-115
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- 2008
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- 2233-7822(pISSN)
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- 2233-7830(eISSN)
Basal cell nevus syndrome: 2 case reports
기저세포모반증훈군 두 증례
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Kim, Jae-Duk
(Department of Oral & Maxillofacial Radiology, College of Dentistry, Chosun University) ;
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Seo, Yo-Seob
(Department of Oral & Maxillofacial Radiology, College of Dentistry, Chosun University) ;
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Kim, Jin-Soo
(Department of Oral & Maxillofacial Radiology, College of Dentistry, Chosun University)
- Published : 2008.06.30
Abstract
The basal cell nevus syndrome (BCNS) is an autosomal dominant disorder, characterized by basal cell carcinomas, odontogenic keratocysts and skeletal abnormalities. We experienced two cases that represented several characteristics of BCNS. Case 1: a thirty three year-old man visited CSU hospital. His radiographs showed four cystic lesions at both maxillary sinus and both mandibular angle, with bifid rib and ectopic calcification of falx cerebri. After marsupialization and enucleation, recurrent and newly developing tendency were found on his follow-up radiographs. Case 2: a seventeen year-old man had four large cystic lesions which were diagnosed as odontogenic keratocysts. He had craniofacial anomalies which included ectopic calcification and frontal bossing.