Pediatric Gastroenterology, Hepatology & Nutrition

The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition (대한소아소화기영양학회)
권호 표지

Primitive Neuroectodermal Tumor of the Liver in a 13-year-old Boy: A Case Report

염증성 거짓 종양으로 오인된 간 내 발생한 원시신경외배엽종양

  • Lee, Sang-Goo (Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Kim, Ji-Eun (Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Lee, Ji-Hyuk (Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Lee, Hye-Jin (Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Lee, Jong-Seung (Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Lee, Jee-Hyun (Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Choe, Yon-Ho (Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine)
  • 이상구 (성균관대학교 의과대학 삼성서울병원 소아과학교실) ;
  • 김지은 (성균관대학교 의과대학 삼성서울병원 소아과학교실) ;
  • 이지혁 (성균관대학교 의과대학 삼성서울병원 소아과학교실) ;
  • 이혜진 (성균관대학교 의과대학 삼성서울병원 소아과학교실) ;
  • 이종승 (성균관대학교 의과대학 삼성서울병원 소아과학교실) ;
  • 이지현 (성균관대학교 의과대학 삼성서울병원 소아과학교실) ;
  • 최연호 (성균관대학교 의과대학 삼성서울병원 소아과학교실)
  • Received : 2008.07.28
  • Accepted : 2008.08.28
  • Published : 2008.09.30
Download PDF
⟨ Previous Next ⟩

Abstract

Primary primitive neuroectodermal tumor (PNET) of the liver is a rare disease with aggressive behavior and poor prognosis. We report a case of a PNET of the liver in a 13-year-old boy. The patient was admitted to the hospital with fever and abdominal pain. Abdominal CT and MRI revealed a 5.5 cm sized, septated, non-enhancing mass in the hepatic hilum. The patient was initially diagnosed with an inflammatory pseudotumor. Despite 9 days of antibiotic therapy, the patient's clinical symptoms did not improve. A liver biopsy was performed in the interest of formulating a differential diagnosis. This procedure revealed tumor cells positive for CD99 on immunohistochemistry. The patient was diagnosed with a PNET.

저자들은 발열과 복부 통증을 주소로 내원한 13세 남자 환자에서 염증성 거짓 종양으로 오인된 간 내 원시신경 외배엽 종양 1예를 경험하였으며 문헌고찰과 함께 보고하는 바이다.

Keywords