Advances in pediatric surgery

Korean Association of Pediatric Surgeons (대한소아외과학회)
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Congenital Sialoblastoma: a Case Report

출생 직후 발견된 선천성 침샘모세포종 1예

  • Moon, Suk-Bae (Department of Pediatric Surgery, Seoul National University Children's Hospital) ;
  • Park, Kwi-Won (Department of Pediatric Surgery, Seoul National University Children's Hospital) ;
  • Jung, Sung-Eun (Department of Pediatric Surgery, Seoul National University Children's Hospital) ;
  • Lee, Seong-Cheol (Department of Pediatric Surgery, Seoul National University Children's Hospital)
  • 문석배 (서울대학교병원 소아외과) ;
  • 박귀원 (서울대학교병원 소아외과) ;
  • 정성은 (서울대학교병원 소아외과) ;
  • 이성철 (서울대학교병원 소아외과)
  • Received : 2008.01.29
  • Accepted : 2008.12.26
  • Published : 2008.12.31
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Abstract

Sialoblastoma is a rare tumor of salivary gland origin, developing in the fetal or neonatal period. Most tumors arise in parotid gland, and rarely in submandibular gland. Because of its rare incidence, diagnosis of the sialoblastoma in head and neck tumors of children is not easy. The case of a congenital submandibular gland sialoblastoma is presented. A neonate was transferred right after birth due to a submandibular mass. CT scan showed a lobulating mass located posterior to the left submandibular gland, suggesting neurogenic tumor or myofibroma. The tumor was excised easily after division of a duct-like structure connecting with the submandibular gland. The microscopic findings showed the basaloid cells and ductules forming cellular nests, separated by thin fibrous tissue. Immunohistochemical staining was positive for cytokeratin, vimentin and Ki-67, which was consistent with sialoblastoma.

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