Papillary Fibroelastoma Originating from the Left Ventricle - A case report -

좌심실에 발생한 유두상 섬유 탄력종 - 1예 보고 -

  • Jeon, Hyun-Woo (Department of Thoracic and Cardiovascular Surgery, The Catholic University of Korea College of Medicine) ;
  • Cho, Kuhn-Hyun (Department of Thoracic and Cardiovascular Surgery, The Catholic University of Korea College of Medicine) ;
  • Wang, Young-Pil (Department of Thoracic and Cardiovascular Surgery, The Catholic University of Korea College of Medicine) ;
  • Kim, Yong-Han (Department of Thoracic and Cardiovascular Surgery, The Catholic University of Korea College of Medicine) ;
  • Lee, Hyun-Seung (Department of Pathology, The Catholic University of Korea College of Medicine) ;
  • Moon, Seok-Whan (Department of Thoracic and Cardiovascular Surgery, The Catholic University of Korea College of Medicine)
  • 전현우 (가톨릭대학교 의과대학 강남성모병원 흉부외과교실) ;
  • 조건현 (가톨릭대학교 의과대학 강남성모병원 흉부외과교실) ;
  • 왕영필 (가톨릭대학교 의과대학 강남성모병원 흉부외과교실) ;
  • 김용한 (가톨릭대학교 의과대학 강남성모병원 흉부외과교실) ;
  • 이현승 (가톨릭대학교 의과대학 강남성모병원 병리학교실) ;
  • 문석환 (가톨릭대학교 의과대학 강남성모병원 흉부외과교실)
  • Published : 2007.11.05

Abstract

Papillary fibroelastoma is a rare benign tumor of the heart. A 21-year-old man presented with dyspnea on exertion and echocardiogram showed a small round mass attached to the anterolateral papillary muscle. After excision of the mass, including anterior papillary muscle, chordae tendinae, and anterior leaflet, he underwent mitral valve re-placement with a mechanical valve. He was discharged on anticoagulant therapy without further problems.

유두상 섬유 탄력종은 심장에 발생하는 양성 종양으로 그 빈도는 매우 드물다. 21세 남자 환자가 운동 시 발생하는 호흡 곤란을 주소로 내원하였고 심초음파상 전측유두근에 위치한 포도알 크기의 심장 종양이 진단되었다. 전신 색전증이 우려되어 응급수술을 통하여 전유두근 및 승모판막에 부착된 종양을 절제하였으며 기계판막으로 승모판치환술을 시행하였다. 환자는 수술 후 항응고제 치료를 받으면서 특별한 문제없이 퇴원하였다.

Keywords

References

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