PET/CT로 혈전증과 감별된 원발성 폐동맥 육종 1례

A Case of Primary Pulmonary Artery Sarcoma Mimicking Pulmonary Embolism: Role of PET/CT for Differential Diagnosis

  • 임상수 (단국대학교 의과대학 내과학교실) ;
  • 홍구현 (단국대학교 의과대학 내과학교실) ;
  • 신재민 (단국대학교 의과대학 내과학교실) ;
  • 김윤섭 (단국대학교 의과대학 내과학교실) ;
  • 지영구 (단국대학교 의과대학 내과학교실) ;
  • 명나혜 (단국대학교 의과대학 병리학교실) ;
  • 박석건 (단국대학교 의과대학 핵의학교실) ;
  • 박재석 (단국대학교 의과대학 내과학교실)
  • Lim, Sang-Soo (Department of Internal Medicine, College of Medicine, Dankook University) ;
  • Hong, Koo-Hyun (Department of Internal Medicine, College of Medicine, Dankook University) ;
  • Shin, Jae-Min (Department of Internal Medicine, College of Medicine, Dankook University) ;
  • Kim, Youn Seup (Department of Internal Medicine, College of Medicine, Dankook University) ;
  • Jee, Young Koo (Department of Internal Medicine, College of Medicine, Dankook University) ;
  • Myoung, Na Hye (Department of Pathology, College of Medicine, Dankook University) ;
  • Park, Seok Gun (Department of Nuclear Medicine, College of Medicine, Dankook University) ;
  • Park, Jae Seuk (Department of Internal Medicine, College of Medicine, Dankook University)
  • 투고 : 2007.01.23
  • 심사 : 2007.02.20
  • 발행 : 2007.03.30

초록

폐동맥 육종은 극히 드문 질환으로 폐동맥 혈전증과 혼동되는 경우가 많다. 육종에서는 FDG 섭취가 증가되므로 $^{18}F-FDG-PET$를 시행하면 FDG 섭취가 없는 색전증과 구별할 수 있지만 해상도가 떨어지는 단점이 있다. 그러므로 CT 영상을 접목한 PET/CT는 폐동맥 육종과 혈전증을 보다 선명하게 구별할 수 있다. 저자들은 혈전증과 감별이 어려운 폐동맥 병변에 대해 PET/CT로 폐동맥 육종의 진단에 도움을 받았던 증례를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Primary pulmonary artery sarcoma is a rare malignant tumor arising from the pulmonary artery. Diagnosis of primary pulmonary artery sarcoma is quite difficult and the conditon is often misdiagnosed as a more common disease, such as a pulmonary embolism. PET can help in diagnosing a pulmonary artery sarcoma due to the increased uptake of $^{18}F-FDG$ in the area of the tumor. However, the poor anatomic resolution of PET has limited its clinical applications in pulmonary vascular disease. The recently developed PET/CT is the fusion of PET and CT that improves the anatomical resolution of PET. We report a case of a primary pulmonary artery sarcoma mimicking a pulmonary embolism that was diagnosed with PET/CT and confirmed with a surgical resection.

키워드

참고문헌

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