이소성 낭성 흉선종 1예

A Case of Ectopic Cystic Thymoma

  • 이재형 (을지의과대학교 을지병원 내과학교실) ;
  • 김일옥 (한양대학교 의과대학 내과학교실) ;
  • 이희경 (한양대학교 의과대학 내과학교실) ;
  • 민경환 (한양대학교 의과대학 병리학교실) ;
  • 김상헌 (한양대학교 의과대학 내과학교실) ;
  • 김태형 (한양대학교 의과대학 내과학교실) ;
  • 손장원 (한양대학교 의과대학 내과학교실) ;
  • 윤호주 (한양대학교 의과대학 내과학교실) ;
  • 신동호 (한양대학교 의과대학 내과학교실) ;
  • 박찬금 (한양대학교 의과대학 병리학교실) ;
  • 강정호 (한양대학교 의과대학 흉부외과학교실) ;
  • 박성수 (한양대학교 의과대학 내과학교실)
  • Lee, Jae Hyung (Department of Internal Medicine, Eulji General Hospital, Eulji University School of Medicine) ;
  • Kim, Il Ok (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Lee, Hee Kyung (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Min, Kyueng Whan (Department of Pathology, College of Medicine, Hanyang University) ;
  • Kim, Sang Heon (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Kim, Tae Hyung (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Sohn, Jang Won (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Yoon, Ho Joo (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Shin, Dong Ho (Department of Internal Medicine, College of Medicine, Hanyang University) ;
  • Park, Chan Kum (Department of Pathology, College of Medicine, Hanyang University) ;
  • Kang, Jung Ho (Department of Thoracic Surgery, College of Medicine, Hanyang University) ;
  • Park, Sung Soo (Department of Internal Medicine, College of Medicine, Hanyang University)
  • 투고 : 2007.01.23
  • 심사 : 2007.04.02
  • 발행 : 2007.04.30

초록

전종격동 하부에 심장과 연접한 이소성 흉선종은 폐암뿐 아니라 흉선종, 생식세포암, 림프종, 전이성 종양 등의 여러 질환과 감별이 필요하다. 병리조직상으로는 이소성 흉선종에 대한 주의가 없는 경우, 미분화상피암, 암성병변의 림프절 전이, 또는 림프구가 우세하게 관찰되는 경우 림프종 등으로 오진될 수도 있으므로 감별진단에 있어 주의가 필요하다. 또한 낭성 흉선종은 이러한 감별진단을 더욱 어렵게 한다. 저자들은 하부 종격동에 심장 우측과 연접하여 발생한 이소성 낭성 흉선종 환자 1예를 경험하였기에 보고하는 바이다.

A thymoma commonly occurs in the superior mediastinum or the upper part of the anterior mediastinum but can be located in other places in rare cases. Cystic degeneration in a thymoma is a relatively common but focal event. In rare cases, the process proceeds to the extent that most if not all of the lesion becomes cystic. We report a case of a patient with a paracardial cystic thymoma in the lower aspect of the anterior mediastinum. A 49-year-old woman was referred to our hospital because of a mass discovered incidentally on a chest X-ray. She showed no symptoms or signs. Contrast-enhanced chest CT scan revealed a $5{\times}5cm$ sized, well-marginated, right paracardial cystic mass with a curvilinear and oval enhancing solid portion. A Surgical resection was performed. The mass was discontinuous with normal thymic tissue. Microscopy revealed a type B1 thymoma with prominent foci of medullary differentiation according to the WHO classification. There was no capsular or local invasion. The postoperative course was uneventful and the patient was discharged in good health.

키워드

참고문헌

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