Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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The Remission of Pure Red Cell Aplasia with a Thymoma after Surgical Resection

수술적 제거로 완치된 순수적혈구 무형성을 동반한 흉선종 1예

  • Kim, Eun Mi (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Kim, Sang-Ha (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Kwon, Woocheol (Department of Radiology, Yonsei University Wonju College of Medicine) ;
  • Kim, Ho Young (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Kim, Chong Whan (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Lee, Bu Ghil (Department of Internal Medicine, Yonsei University Wonju College of Medicine) ;
  • Jung, Soon-Hee (Department of Pathology, Yonsei University Wonju College of Medicine) ;
  • Lee, Chong Kook (Department of Thoracic and Cardiovascular Surgery, Yonsei University Wonju College of Medicine) ;
  • Yong, Suk Joong (Department of Internal Medicine, Yonsei University Wonju College of Medicine)
  • 김은미 (연세대학교 원주의과대학 내과학교실) ;
  • 김상하 (연세대학교 원주의과대학 내과학교실) ;
  • 권우철 (연세대학교 원주의과대학 영상의학과교실) ;
  • 김호영 (연세대학교 원주의과대학 내과학교실) ;
  • 김종환 (연세대학교 원주의과대학 내과학교실) ;
  • 이부길 (연세대학교 원주의과대학 내과학교실) ;
  • 정순희 (연세대학교 원주의과대학 병리학교실) ;
  • 이종국 (연세대학교 원주의과대학 흉부외과학교실) ;
  • 용석중 (연세대학교 원주의과대학 내과학교실)
  • Received : 2007.08.31
  • Accepted : 2007.10.29
  • Published : 2007.11.30
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Abstract

Thymomas are associated with different paraneoplastic syndromes, with the most clinically important association being with myasthenia gravis, hypogammaglobulinemia, and pure red cell aplasia (PRCA). The optimal therapy for PRCA that complicates a thymoma is unknown, given the rarity of the clinical situation. It has been suggested that remission following surgery alone is uncommon and most patients will require some other form of therapy. We report a case of PRCA with a thymoma in a 59-year-old man who remained in complete remission of the PRCA after surgical resection of the thymoma.

저자들은 심한 빈혈에 의한 전신무력감과 어지러움 증상을 주소로 내원한 환자에서 전종격동 종양이 관찰되어 조직검사를 시행하였으며, 흉선종에 동반된 PRCA로 진단하였다. 치료를 위해 흉선종 적출을 시행하였으며 수술 후 1년 6개월까지 더 이상의 수혈 없이 혈색소가 11.0g/dL 이상으로 유지되어 수술적 제거를 통한 흉선종에 동반된 PRCA의 완치를 경험하였다.

Keywords

References

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