Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
권호 표지

Chest Wall Lipoblastoma in a Nineteen-months-old Boy -A case report-

19개월 된 남아에서 발견된 흉벽 내 지방모세포종 - 1예 보고 -

  • Lee, Jong-Mo (Department of Thoracic and Cardiovascular Surgery, Daejeon St. Mary's Hospital, The Catholic University of Korea College of Medicine) ;
  • Kwon, Jong-Bum (Department of Thoracic and Cardiovascular Surgery, Daejeon St. Mary's Hospital, The Catholic University of Korea College of Medicine) ;
  • Moon, Mi-Hyoung (Department of Thoracic and Cardiovascular Surgery, Kangnam St. Mary's Hospital, The Catholic University of Korea College of Medicine) ;
  • Park, Kuhn (Department of Thoracic and Cardiovascular Surgery, Daejeon St. Mary's Hospital, The Catholic University of Korea College of Medicine)
  • 이종호 (가톨릭대학교 의과대학 대전성모병원 흉부외과학교실) ;
  • 권종범 (가톨릭대학교 의과대학 대전성모병원 흉부외과학교실) ;
  • 문미형 (가톨릭대학교 의과대학 강남성모병원 흉부외과학교실) ;
  • 박건 (가톨릭대학교 의과대학 대전성모병원 흉부외과학교실)
  • Published : 2007.05.05
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Abstract

Lipoblastoma is a rare benign mesenchymal tumor that occurs primarily in infancy and childhood. There are two types of lipoblastoma: focal or diffuse (lipoblastomatosis). This is typically located in the extremities, and less frequently in the trunk, head and neck, and the retroperitoneum. Lipoblastoma is a tumor with a good prognosis with no reported metastasis, despite of its potential for local invasion, local recurrence and rapid growth. Complete surgical resection is essential for treatment, and long term follow up is needed.

지방모세포종은 드문 양성, 간질기원의 종양으로 주로 유아 및 소아에서 발생한다. 국한형과 미만형의 두 종류가 있으며 전형적으로 사지에서 발생하고, 그 밖에 체간, 두경부, 그리고 후복막강에서 발생한다. 지방모세포종은 국소 침윤 및 재발하는 성질이 있으며, 빠르게 성장하지만, 아직 전이된 예가 보고된 적이 없는, 예후가 좋은 종양이다. 완전 절제가 필요하며, 장기적인 추적관찰이 필요하다.

Keywords

References

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