Clinical and Experimental Pediatrics

대한소아청소년과학회 (The Korean Pediatric Society)
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다발성 신외 증상이 동반된 용혈요독증후군 1례

Multiple extrarenal manifestations in hemolytic uremic syndrome: A case report

  • 김유진 (가톨릭대학교 의과대학 소아과학교실) ;
  • 김소영 (가톨릭대학교 의과대학 소아과학교실)
  • Kim, Eugene (Department of Pediatrics, College of Medicine, Catholic University) ;
  • Kim, So-Young (Department of Pediatrics, College of Medicine, Catholic University)
  • 투고 : 2007.11.15
  • 심사 : 2007.12.10
  • 발행 : 2007.12.15
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초록

근래 용혈요독증후군의 신외 증상에 대한 인식이 점점 더 증가하고 있으며 이환률과 사망률의 주요 결정인자가 되고 있다. 용혈요독증후군 환자의 심장동맥순환계에서 미소혈전이 발견되는 일은 흔하지만 실제 임상적으로 명백하게 발현하는 폐 혹은 심장 합병증은 흔하지 않다. 저자들은 용혈요독증후군으로 치료 받던 10개월 영아에서 폐출혈, 급성호흡곤란증후군, 확장심근병증 등이 발생하여 지지요법 후 회복된 1례를 경험하여 문헌고찰과 함께 보고하는 바이다.

Extrarenal manifestations of hemolytic uremic syndrome (HUS) have increasingly been recognized and may be major determinants of mortality and morbidity. Although microthrombi are often found in the pulmonary and coronary circulation, apparent lung and cardiac involvement are clinically infrequent. We describe here a 10-month-old boy with HUS who developed pulmonary hemorrhage, acute respiratory distress syndrome and dilated cardiomyopathy. Complete renal as well as clinical recovery from these very uncommon complications was achieved by optimum supportive care.

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참고문헌

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