Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Tracheobronchomegaly with Pneumonia

폐렴을 동반한 기관 및 주기관지의 확장 소견

  • Joo, Kyu Re (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Oak, Ju Hyun (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Lee, Sung Eun (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Jang, Suk Tae (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Kim, Sung Kyoung (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Lee, Sang Haak (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Song, Jeong Sup (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Park, Sung Hak (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Moon, Hwa Sik (Department of Internal Medicine, The Catholic University of Korea, College of Medicine) ;
  • Lee, Bae Young (Department of Radiology, The Catholic University of Korea, College of Medicine) ;
  • Kim, Hyeon Sook (Department of Radiology, The Catholic University of Korea, College of Medicine)
  • 주겨레 (가톨릭대학교 의과대학 내과학교실) ;
  • 옥주현 (가톨릭대학교 의과대학 내과학교실) ;
  • 이성은 (가톨릭대학교 의과대학 내과학교실) ;
  • 장석태 (가톨릭대학교 의과대학 내과학교실) ;
  • 김성경 (가톨릭대학교 의과대학 내과학교실) ;
  • 이상학 (가톨릭대학교 의과대학 내과학교실) ;
  • 송정섭 (가톨릭대학교 의과대학 내과학교실) ;
  • 박성학 (가톨릭대학교 의과대학 내과학교실) ;
  • 문화식 (가톨릭대학교 의과대학 내과학교실) ;
  • 이배영 (가톨릭대학교 의과대학 방사선과학교실) ;
  • 김현숙 (가톨릭대학교 의과대학 방사선과학교실)
  • Received : 2006.06.16
  • Accepted : 2006.07.18
  • Published : 2006.10.30
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Abstract

A 66-years-old man was refered to our hospital because of cough, sputum, chill and fever. Enlargement of the trachea and main bronchi on radiography and bronchoscopy is compatible with Mounier-Kuhn syndrome. Mounier-Kuhn syndrome or tracheobronchomegaly is a rare disorder of uncertain etiology, characterized by marked dilatation of the trachea and major bronchi. This syndrome is associated with tracheal diverticulosis, bronchiectasis and recurrent respiratory tract infection. We report a rare case of Mounier-Kuhn syndrome with pneumonia and literature reviews.

저자들은 폐렴을 동반한 기도의 드문 질환인 Mounier-Kuhn syndrome을 가진 환자의 단순흉부방사선, 기도내시경 소견과 함께 고식적인 흉부 전산화 단층 촬영을 시행 후 3차원적인 입체 영상으로 재구성한 소견을 고찰과 함께 1예 보고하는 바이다.

Keywords

References

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