Anomalous systemic arterial supply to lung without sequestration in an infant who has congenital heart disease : a case report

선천성 심장질환을 가진 영아에서 발견된 폐 격리증을 동반하지 않은 폐의 이상 체 동맥 기시 1례

  • Jang, Yeon Woo (Division of Pediatric Cardiology, Heart Center, Gil Medical Center, Gachon Medical School) ;
  • Choi, Duck Young (Division of Pediatric Cardiology, Heart Center, Gil Medical Center, Gachon Medical School)
  • 장연우 (가천의과대학교 길병원 심장센터 소아심장과) ;
  • 최덕영 (가천의과대학교 길병원 심장센터 소아심장과)
  • Received : 2006.04.03
  • Accepted : 2006.05.11
  • Published : 2006.08.15

Abstract

Systemic arterial supply from the aorta to the lung is a rare congenital anomaly within the spectrum of bronchopulmonary sequestration according to Pryce's terminology. We describe our experience of this anomaly in an infant with congenital cardiac disease confirmed by multidetector CT scan. We found a systemic arterial supply from the aorta to the right lower lobe of lung without right lower lobar pulmonary artery and bronchopulmonary sequestration. This combination of congenital anomaly is most rare form.

폐 격리증이 없는 정상적인 폐에 체 혈관이 이상 기시하는 것은 매우 드문 질환이다. 저자들은 반복적인 하기도 감염을 보이는 영아에서 선천성 심장질환의 상태가 본 하기도 감염을 나타낼 정도로 심하지 않음을 이상히 여겨 컴퓨터 단층 촬영을 시행하였다. 그 결과 폐 격리증이 없는 폐의 이상 체 동맥 기시가 우측 폐하 엽에 존재함과 동시에 우측 하엽 폐동맥이 없는 사실을 확인하게 되었다. 어린 나이에 이 같은 선천성 질환의 조합은 이전에 보고 된 바가 없는 매우 드문 질환으로 생각된다.

Keywords

References

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