Journal of Korean Neurosurgical Society

  • 제39권6호
  • /
  • Pages.459-463
  • /
  • 2006
  • /
  • 2005-3711(pISSN)
  • /
  • 1598-7876(eISSN)
대한신경외과학회 (The Korean Neurosurgical Society)
권호 표지

Diffuse Neurofibroma Presenting with Spontaneous Intra-Tumoral Hemorrhage

  • Kwak, Seung-Won (Department of Neurosurgery, Our Lady of Mercy Hospital, College of Medicine, The Catholic University of Korea) ;
  • Han, Young-Min (Department of Neurosurgery, Our Lady of Mercy Hospital, College of Medicine, The Catholic University of Korea) ;
  • Park, Young-Sup (Department of Neurosurgery, Our Lady of Mercy Hospital, College of Medicine, The Catholic University of Korea)
  • 발행 : 2006.06.30
PDF 다운로드
⟨ 이전 논문 다음 논문 ⟩

초록

This report describes a case of diffuse neurofibroma[DNF] that presented with spontaneous intratumoral hemorrhage. A 31-year-old man with cutaneous manifestations typical of neurofibromatosis type 1[NF1] was referred to hospital with a progressively expanding scalp swelling. Magnetic resonance imaging[MRI] showed an acute hematoma surrounded by a dense mass on the parietooccipital scalp. Plain skull radiographs and a computed tomography[CT] scan revealed bony defects in the occipital bone around the lambdoid suture and the skull base, including the sphenoid and petrous bones. The tumor extended to the upper cervical region and infiltrated through the fascia of the musculature. The tumor and adjacent soft tissue were highly vascular, which made surgical resection difficult. We describe the clinical, radiological and pathological features of this patient md discuss the surgical methods used to avoid a life-threatening hemorrhage during surgery.

키워드

참고문헌

  1. De Varebeke SJ, De Schepper A, Hauben E, Declau F, van Marck E, van de Heyning PH : Subcutaneous diffuse neurofibroma of the neck : a case report. J Laryngol Otol 110 : 182-184, 1996
  2. Jacquemin C, Bosley TM, Liu D, Svedberg H, Buhaliqa A : Reassessment of sphenoid dysplasia associated with neurofibromatosis type 1. AJNR Am J Neuroradiol 23 : 644-648, 2002
  3. Khan AK, Deb S, Ray DK, Mandal SN, Mukhopadhaya S, Mandal S : Diffuse neurofibroma of scalp. Neurol India 50 : 516-517, 2002
  4. Kloos RT, Rufini V, Gross MD, Shapiro B : Bone scans in neurofibromatosis : neurofibroma, plexiform neuroma and neurofibrosarcoma. J Nucl Med 37 : 1778-1783, 1996
  5. Lin YC, Chen HC : Rare complication of massive hemorrhage in neurofibromatosis with arteriovenous malformation. Ann Plast Surg 44 : 221-224, 2000 https://doi.org/10.1097/00000637-200044020-00016
  6. Macfarlane R, Levin AV, Weksberg R, Blaser S, Rutka JT : Absence of the greater sphenoid wing in neurofibromatosis type I : congenital or acquired : case report. Neurosurgery 37 : 129-133, 1995 https://doi.org/10.1227/00006123-199507000-00020
  7. Park SK, Yoo MJ, Hahn YS, Yoo TJ, Lee KC, Lee HJ : A case of pulsating exophthalmos due to defective development of the sphenoid bone with plexiform neurofibroma. J Korean Neurosurg Soc 6 : 163-168, 1977
  8. Peh WCG, Shek TWH, Yip DKH : Magnetic resonance imaging of subcutaneous diffuse neurofibroma. Br J Radiol 70 : 1180-1183, 1997 https://doi.org/10.1259/bjr.70.839.9536912
  9. Sawada Y : Hemorrhage into a plexiform neurofibroma induced by trauma : a rare complication of von Recklinghausen's disease. J Dermatol 14 : 378-381, 1987 https://doi.org/10.1111/j.1346-8138.1987.tb03596.x
  10. Tung TC, Chen YR, Chen KT, Chen CT, Bendor-Samuel R : Massive intratumor hemorrhage in facial plexiform neurofibroma. Head Neck 19 : 158-162, 1997 https://doi.org/10.1002/(SICI)1097-0347(199703)19:2<158::AID-HED13>3.0.CO;2-9
  11. Van Zuuren EJ, Posma AN : Diffuse neurofibroma on the lower back. J Am Acad Dermatol 48 : 938-940, 2003 https://doi.org/10.1067/mjd.2003.141