Journal of Korean Neurosurgical Society

The Korean Neurosurgical Society (대한신경외과학회)
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Familial Idiopathic Basal Ganglia Calcification

  • Shin, Dong-Ah (Department of Neurosurgery, Yonsei University College of Medicine) ;
  • Gong, Tae-Sik (Department of Neurosurgery, Presbyterian Medical Center) ;
  • Shin, Dong-Gyu (Department of Neurosurgery, Presbyterian Medical Center) ;
  • Kim, Hyoung-Ihl (Department of Neurosurgery, Presbyterian Medical Center)
  • Published : 2006.09.30
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Abstract

Familial idiopathic basal ganglia calcification[FIBGC] is an inheritable neurological condition characterized by calcium deposits in the basal ganglia and extra-basal ganglia areas. The condition manifests as parkinsonism and other variable neuropsychiatric symptoms. FIBGC is a rare condition, and its pathophysiology has not yet been fully elucidated. Here we report the results of a clinical study of two related patients diagnosed with FIBGC.

Keywords

References

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