Clinical and Experimental Pediatrics

The Korean Pediatric Society (대한소아청소년과학회)
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A Case of Congenital Laryngeal Atresia with Single Umbilical Artery Who Required a Tracheotomy

기관절개술을 받았던 단일 제대동맥이 동반된 선천성 후두폐쇄증 1례

  • Wi, Ho Sung (Department of Pediatrics, College of Medicine, Hanyang University) ;
  • Baek, Hey Sung (Department of Pediatrics, College of Medicine, Hanyang University) ;
  • Oh, Jae Won (Department of Pediatrics, College of Medicine, Hanyang University) ;
  • Yum, Myung-Kul (Department of Pediatrics, College of Medicine, Hanyang University) ;
  • Kim, Yong Joo (Department of Pediatrics, College of Medicine, Hanyang University) ;
  • Moon, Soo Jee (Department of Pediatrics, College of Medicine, Hanyang University) ;
  • Tae, Kyung (Department of Otolaryngology, College of Medicine, Hanyang University) ;
  • Kim, Chang-Ryul (Department of Pediatrics, College of Medicine, Hanyang University)
  • 위호성 (한양대학교 의과대학 소아과학교실) ;
  • 백혜성 (한양대학교 의과대학 소아과학교실) ;
  • 오재원 (한양대학교 의과대학 소아과학교실) ;
  • 염명걸 (한양대학교 의과대학 소아과학교실) ;
  • 김용주 (한양대학교 의과대학 소아과학교실) ;
  • 문수지 (한양대학교 의과대학 소아과학교실) ;
  • 태경 (한양대학교 의과대학 이비인후과학교실) ;
  • 김창렬 (한양대학교 의과대학 소아과학교실)
  • Received : 2004.11.26
  • Accepted : 2005.01.12
  • Published : 2005.05.15
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Abstract

Congenital laryngeal atresia is a rare cause of airway obstruction that is almost always lethal within a few minutes after birth. Therefore congenital laryngeal atresia should be diagnosed in the prenatal period. If not, it should be considered in newborn infant with life-threatening symptoms at birth such as cyanosis and dyspnea that need emergent procedures like a tracheotomy. We report a case of congenital laryngeal atresia with single umbilical artery diagnosed in a one-day-old neonate who required a tracheotomy and ventilator care after intubation failure.

재태 연령 38주, 출생체중 3,040 g, 제왕절개로 출생하여 단 일제대동맥이 동반되고 첫 울음 없이 전신에 청색증, 심한 호흡 곤란이 발생하여 기관내삽관을 시행하였으나 실패 한 후 후두내시경을 통해 확진된 선천성 후두폐쇄증 1례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.

Keywords

References

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