Taussig-Bing Anomaly with Coarctation of Aorta

대동맥 축착을 동반한 Taussig-Bing 기형의 수술 치험 1예

  • Kim, Hyuck (Dept. of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University) ;
  • Lim, Hyoun-Soo (Dept. of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University) ;
  • Kim, Young-Hak (Dept. of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University) ;
  • Chung, Won-Sang (Dept. of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University) ;
  • Kang, Jung-Ho (Dept. of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University) ;
  • Lee, Chul-Beom (Dept. of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University) ;
  • Jee, Heng-Ok (Dept. of Thoracic and Cardiovascular Surgery, College of Medicine, Hanyang University) ;
  • Kim, Nam-Su (Depat. of Pediatric Cardiology, College of Medicine, Hanyang University)
  • 김혁 (한양대학교 의과대학 흉부외과학교실) ;
  • 임현수 (한양대학교 의과대학 흉부외과학교실) ;
  • 김영학 (한양대학교 의과대학 흉부외과학교실) ;
  • 정원상 (한양대학교 의과대학 흉부외과학교실) ;
  • 강정호 (한양대학교 의과대학 흉부외과학교실) ;
  • 이철범 (한양대학교 의과대학 흉부외과학교실) ;
  • 지행옥 (한양대학교 의과대학 흉부외과학교실) ;
  • 김남수 (한양대학교 의과대학 소아과학교실)
  • Published : 2003.03.01

Abstract

The patient was a 30-day-old female infant with symptoms of severe dyspnea and cyanosis, when she was admitted to the ER. The echocardiography revealed DORV with subpulmonary VSD, and the diagnosis of Taussig-Bing anomaly was made. Two days after admission, an urgent operation was performed. The operation consisted of intraventricular tunnel repair and arterial switch operation. She was discharged, and after checking her chest X-ray through OPD, there was no interval change of cardiomegaly. She was then re-admitted, and the angiography revealed coactation of aorta. We performed a resection and end-to-end anastomosis of aorta. She is currently in good condition 11 months postoperatively.

생후 30일된 환아로 심한 호흡곤란과 청색증을 주소로 본인 응급실로 이송되었다. 심초음파상 Taussig-Bing 기형으로 진단되어 입원 2일째 긴급 수술을 하였다. 수술은 심실중격 결손을 혈류가 좌심실에서 폐동맥으로 가도록 복원하고 대동맥 전위술을 하였다. 퇴원 후 외래에서 시행한 단순 흉부촬영상 심비대의 유의한 감소가 없어 재입원을 한 후 심혈관 촬영술을 하였고, 대동맥 축착이 추가로 관찰되었다. 이에 대한 교정술을 하였으며, 환아는 큰 문제없이 회복되어 11개월 간 추적 관찰 중이다.

Keywords

References

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