Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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Idiopathic Fibrosing Mediastinitis Causing Extensive Fibrotic Veno-occlusion with Minimal Mediastinal Involvement

광범위한 섬유성 정맥 폐쇄를 동반한 특발성 섬유화성 종격동염 1예

  • Kim, Je-Hyeong (Department of Internal Medicine, College of Medicine, Korea University) ;
  • Hur, Gyu-Young (Department of Internal Medicine, College of Medicine, Korea University) ;
  • Lee, Seung-Heon (Department of Internal Medicine, College of Medicine, Korea University) ;
  • Lee, Sang-Yeub (Department of Internal Medicine, College of Medicine, Korea University) ;
  • Park, Sang-Myun (Department of Pathology, College of Medicine, Korea University) ;
  • Shin, Chol (Department of Internal Medicine, College of Medicine, Korea University) ;
  • Shim, Jae-Jeong (Department of Internal Medicine, College of Medicine, Korea University) ;
  • In, Kwang-Ho (Department of Internal Medicine, College of Medicine, Korea University) ;
  • Kim, Han-Kyeom (Department of Pathology, College of Medicine, Wonkwang University) ;
  • Kang, Kyung-Ho (Department of Internal Medicine, College of Medicine, Korea University) ;
  • Yoo, Se-Hwa (Department of Internal Medicine, College of Medicine, Korea University)
  • 김제형 (고려대학교 의과대학 내과학교실) ;
  • 허규영 (고려대학교 의과대학 내과학교실) ;
  • 이승헌 (고려대학교 의과대학 내과학교실) ;
  • 이상엽 (고려대학교 의과대학 내과학교실) ;
  • 박상면 (원광대학교 의과대학 내과학교실) ;
  • 신철 (고려대학교 의과대학 내과학교실) ;
  • 심재정 (고려대학교 의과대학 내과학교실) ;
  • 인광호 (고려대학교 의과대학 내과학교실) ;
  • 김한겸 (고려대학교 의과대학 병리학교실) ;
  • 강경호 (고려대학교 의과대학 내과학교실) ;
  • 유세화 (고려대학교 의과대학 내과학교실)
  • Published : 2002.03.30
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Abstract

A 68-year-old woman was admitted after suffering facial edema with neck vein engorgement for approximately 2 months. A chest X-ray showed a mild widening of the superior mediastinum and a luminal obliteration of the superior vena cava(SVC) was noted on a computed tomograph. Venography showed that both subclavian veins were obstructed at the level of the proximal clavicle with a nonvisualization of the SVC. The SVC, both the innominate and the left internal jugular veins were completely obstructed with extensive cord-like fibrotic changes despite the absence of mediastinal involvement. The microscopic features showed a chronic granulomatous inflammation with a fibrosis minimally invading the mediastinal fat, which is consistent with fibrosing mediastinitis.

특발성 섬유화성 종격동염은 일반적으로 일차적인 종격동의 섬유화 및 석회화가 종격동 기관을 침범하거나 압박함으로써 상대정맥증후군 등의 임상양상을 나타내는 질환이다. 그러나 저자등은 종격동의 침범은 아주 경미하면서도 광범위하고 심한 종격동 혈관의 섬유성 폐쇄를 동반한 특발성 섬유화성 종격동염 1예를 경험하였기에 보고하는 바이다.

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