A Case of Respiratory Difficulty Due to Congenital Tracheal Calcification and Nasal Pyriform Aperture Stenosis

선천성 기관 석회화와 조롱박 구멍 협착 (Nasal Pyriform Aperture Stenosis)에 의한 호흡 곤란증 1례

  • Kim, Kyu Tae (Department of Pediatrics, College of Medicine, Pusan National University) ;
  • Kim, Young Mi (Department of Pediatrics, College of Medicine, Pusan National University) ;
  • Park, Su Eun (Department of Pediatrics, College of Medicine, Pusan National University) ;
  • Park, Jae Hong (Department of Pediatrics, College of Medicine, Pusan National University) ;
  • Noh, Hawn Jung (Department of Otolaryngology, College of Medicine, Pusan National University) ;
  • Kim, Hak Jin (Department of Radiology, College of Medicine, Pusan National University)
  • 김규태 (부산대학교 의과대학 소아과학교실) ;
  • 김영미 (부산대학교 의과대학 소아과학교실) ;
  • 박수은 (부산대학교 의과대학 소아과학교실) ;
  • 박재홍 (부산대학교 의과대학 소아과학교실) ;
  • 노환중 (부산대학교 의과대학 이비인후과학교실) ;
  • 김학진 (부산대학교 의과대학 방사선과학교실)
  • Received : 2001.01.11
  • Accepted : 2002.01.31
  • Published : 2002.05.15

Abstract

Nasal obstruction is a cause of respiratory distress in newborns. The congenital nasal airway obstructive abnormalities are classified into three forms according to the location: posterior choanal atresia, nasal cavity stenosis and congenital nasal pyriform aperture stenosis(CNPAS). CNPAS is located at the anterior part of the nasal fossa. CT is the study of choice to make the diagnosis of CNPAS and rule out other causes of nasal obstruction. Though conservative management of CNPAS is recommended, in cases of severe CNPAS surgical treatment should be considered. Calcification of cartilage in the larynx, trachea and bronchi is extremely rare in children. Such calcifications are generally discovered in young children with congenital stridor. The clinical course is favorable. No case with CNPAS and tracheal calcification is reported in newborn. We report a one-day-old girl with CNPAS and tracheal calcification who presented with respiratory difficulty immediately after birth.

저자들은 출생 후 수 시간 뒤에 발생한 호흡 곤란을 주소로 내원한 환아에서 우연히 발견된 기관의 석회화와 양측 조롱박 구멍 협착증을 진단하고 비강 내에 스텐트를 위치시키는 수술로서 호흡 곤란 등의 증상 호전된 환아를 보고하는 바이다.

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