Clinical and Experimental Pediatrics
- Volume 45 Issue 10
- /
- Pages.1292-1298
- /
- 2002
- /
- 2713-4148(eISSN)
A Case of Melkersson-Rosenthal Syndrome
Melkersson-Rosenthal 증후군 1례
- Pee, Dae Hun (Department of Pediatrics, College of Medicine, Korea University) ;
- Na, Yo Won (Department of Pediatrics, College of Medicine, Korea University) ;
- Chang, Ki Young (Department of Pediatrics, College of Medicine, Korea University) ;
- Seo, Woo Keun (Department of Neurology, College of Medicine, Korea University) ;
- Lee, Kee Hyoung (Department of Pediatrics, College of Medicine, Korea University) ;
- Eun, Baik-Lin (Department of Pediatrics, College of Medicine, Korea University)
- 피대훈 (고려대학교 의과대학 소아과학교실) ;
- 나요원 (고려대학교 의과대학 소아과학교실) ;
- 장기영 (고려대학교 의과대학 소아과학교실) ;
- 서우근 (고려대학교 의과대학 신경과학교실) ;
- 이기형 (고려대학교 의과대학 소아과학교실) ;
- 은백린 (고려대학교 의과대학 소아과학교실)
- Received : 2002.05.02
- Accepted : 2002.07.15
- Published : 2002.10.15
Abstract
Melkersson-Rosenthal syndrome(MRS) is a rare disorder, having a symptom triad of recurrent facial palsy, orofacial swelling and fissured tongue(lingua plicata). This disorder is usually recurrent or progressive, and monosymptomatic or oligosymptomatic forms have been reported to be more common than classic forms. Generally, MRS occurs in young adults at the end of the second decade of life and incidence of the disease in childhood is known to be very low. Although the clinical manifestation of MRS in children is similar to that in adults, early diagnosis and management is essential to avoid long-lasting functional disorders and psychological problems. We experienced MRS in a 13 year old boy with a history of recurrent facial palsy. We report this case with review of related literature.
저자들은 반복적인 안면 신경 마비의 과거력을 가진 환아에서 좌측 안면부의 부종과 함께 나타난 Melkersson-Rosenthal 증후군 증례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.