A case of Acute Autonomic and Sensory Neuropathy

급성 자율 감각 신경병증 1례

  • Lee, Jong-Mun (Department of Neurology, Medical Collage, Korea University) ;
  • Kwon, Do-Young (Department of Neurology, Medical Collage, Korea University) ;
  • Koh, Seong-Beom (Department of Neurology, Medical Collage, Korea University) ;
  • Kim, Byung-Jo (Department of Neurology, Medical Collage, Korea University) ;
  • Park, Min-Kyu (Department of Neurology, Medical Collage, Korea University) ;
  • Park, Kun-Woo (Department of Neurology, Medical Collage, Korea University) ;
  • Lee, Dae-Hie (Department of Neurology, Medical Collage, Korea University)
  • 이종문 (고려대학교 의과대학 신경과학교실) ;
  • 권도영 (고려대학교 의과대학 신경과학교실) ;
  • 고성범 (고려대학교 의과대학 신경과학교실) ;
  • 김병조 (고려대학교 의과대학 신경과학교실) ;
  • 박민규 (고려대학교 의과대학 신경과학교실) ;
  • 박건우 (고려대학교 의과대학 신경과학교실) ;
  • 이대희 (고려대학교 의과대학 신경과학교실)
  • Published : 2002.05.01

Abstract

Acute autonomic neuropathy is a rare disease. Since the first case was reported by Young et.al., in 1969, a number of similar cases have been described, with some variation of the accompanied neurologic deficits. Acute autonomic and sensory neuropathy(AASN) is characterized by the acute onset of autonomic dysfunction and sensory disturbances. A 16-year-old girl experienced high fever($40^{\circ}C$) and erythematous rash on whole trunk and face followed by pain and sensory loss over the whole body, dysphagia, ataxia, urinary retention, and postural hypotension. There was no evidence of limb weakness. The electrophysiologic studies of this patient revealed sensory polyneuropathy and the various autonomic function test showed autonomic dysfunction. The recovery of her autonomic and sensory symptoms is incomplete, three months after the onset of the symptoms. The etiology of the acute autonomic and sensory neuropathy is not known. Most previous authors have suggested the dysautonomia may be an acute immunological damage to peripheral fibers of the autonomic nervous system. We report a case of acute autonomic and sensory neuropathy.

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